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Portosystemic Shunt with Polysplenia and Hypoplastic Left Heart Syndrome

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Abstract

We report a unique case of portosystemic shunt with polysplenia and hypoplastic left heart syndrome. The abnormal vessel connected the right renal vein and the splenic vein. The shunt flow was from the systemic vein to the portal vein before the Fontan-type operation, but it reversed and ran from portal vein to systemic vein after the Fontan-type operation.

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Authors and Affiliations

  1. Division of Pediatric Cardiology, Chiba Children's Hospital, 579-1 Heta-cho, Midori-ku, Chiba, Japan

    H. Ikeda, H. Aotsuka, H. Nakajima & M. Sawada

Authors
  1. H. Ikeda
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  2. H. Aotsuka
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  3. H. Nakajima
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  4. M. Sawada
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Correspondence to H. Ikeda.

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Ikeda, H., Aotsuka, H., Nakajima, H. et al. Portosystemic Shunt with Polysplenia and Hypoplastic Left Heart Syndrome. Pediatr Cardiol 26, 446–448 (2005). https://doi.org/10.1007/s00246-004-0737-y

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  • DOI: https://doi.org/10.1007/s00246-004-0737-y

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