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Kombinierte Pulmonal- und Aortenstenose

Plötzlicher Tod eines eineinhalbjährigen Mädchens

Combined pulmonary and aortic stenoses

Sudden death of an 18-month-old girl

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Zusammenfassung

Aortenstenosen werden bei 3–6% der Kinder mit kongenitalen Vitien festgestellt; plötzliche Todesfälle ereignen sich bei 1% der Kinder mit Aortenstenose/Jahr. Die Kombination einer Aorten- mit einer gleichzeitigen Pulmonalstenose ist relativ selten. Vorgestellt wird der Todesfall eines eineinhalb Jahre alt gewordenen Mädchens, das plötzlich bei valvulärer Aorten- und Pulmonalklappenstenose mit Klappendysplasie verstarb.

Abstract

Aortic stenoses are found in 3–6% of children with congenital cardiac malformation and sudden death occurs in 1% of children with an aortic stenosis per year. The combination of valvular aortic stenosis with valvular pulmonary stenosis is a comparatively rare finding. The case of sudden death of an 18-month-old girl with aortic and pulmonary valvular stenoses and valvular dysplasia is presented.

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Authors and Affiliations

  1. Institut für Rechtsmedizin, Universität Bonn, Stiftsplatz 12, 53111, Bonn, Deutschland

    B. Madea, G. Arneke, C. Schyma & R. Amberg

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  1. B. Madea
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  2. G. Arneke
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  3. C. Schyma
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  4. R. Amberg
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Correspondence to B. Madea.

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Madea, B., Arneke, G., Schyma, C. et al. Kombinierte Pulmonal- und Aortenstenose. Rechtsmedizin 22, 178–182 (2012). https://doi.org/10.1007/s00194-012-0824-y

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  • DOI: https://doi.org/10.1007/s00194-012-0824-y

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