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Ebstein’s anomaly of the tricuspid valve

  • Congenital Heart Disease
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Abstract

Ebstein’s anomaly of the tricuspid valve is a rare lesion comprising less than 1% of patients with congenital heart disease. Among congenital heart lesions, Ebstein’s anomaly is one of the most diverse in presentation, severity, and management. In its most severe form, it is also one of the most lethal. In this article we present a case of a patient who developed cardiac symptoms in adulthood. We follow this with a review of the pathology, clinical presentation, evaluation, and management of Ebstein’s anomaly.

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Authors and Affiliations

  1. Division of Cardiology, University of Washington, 1959 NE Pacific, Box 356422, 98105, Seattle, WA, USA

    Michelle Gurvitz MD

Authors
  1. Michelle Gurvitz MD
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  2. Karen Stout MD
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Correspondence to Michelle Gurvitz MD.

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Gurvitz, M., Stout, K. Ebstein’s anomaly of the tricuspid valve. Curr Cardiol Rep 9, 336–342 (2007). https://doi.org/10.1007/BF02938383

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