Abstract
A patient having type IV Ehlers-Danlos syndrome is described because of an uncommon combination of malformations. He had multiple aneurysms, a hepatic artery-to-portal vein fistula, and diverticula of the biliary passages, the sigmoid colon, and bladder. He also suffered from scoliosis and dilatation of inner and outer cerebral spinal fluid containing spaces.
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Kahn, T., Reiser, M., Gmeinwieser, J. et al. The Ehlers-Danlos syndrome, type IV, with an unusual combination of organ malformations. Cardiovasc Intervent Radiol 11, 288–291 (1988). https://doi.org/10.1007/BF02577038
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DOI: https://doi.org/10.1007/BF02577038