Summary
Cardiac catheterization was performed in nine patients with unilateral absence of a pulmonary artery. Aortography revealed a diverticulum of the innominate artery in five of six patients in whom the aortic arch and absent pulmonary artery were on opposite sides. It is suggested that the diverticulum indicates fetal systemic blood supply to the affected lung through the distal part of the sixth aortic arch, which—consisting of ductal tissue—obliterated after birth, leaving the diverticulum where the ductus joins the innominate artery.
Similar content being viewed by others
References
Cucci CE, Domle EF, Lewis EW Jr (1964) Absence of a primary division of the pulmonary trunk: An ontogenetic theory.Circulation 29:124–131
Heintzen P, Teske I (1960) Die einseitige Agenesie der Lungenarterie.Arch Kreislaufforsch 32:263–291
Heintzen P (1966) Einseitige Lungenarterienagenesie, in Opitz H, Schmid F (eds):Handbuch der Kinderheilkunde. Berlin, vol 7, pp 515–519
Kauffman SL, Yao AC, Webber CB, Lynfield J (1967) Origin of the right pulmonary artery from the aorta.Am J Cardiol 19:741–748
McKim JS, Wiglesworth FW (1954) Absence of the left pulmonary artery.Am Heart J 47:845–859
Pool PE, Vogel JHK, Blount SG (1962) Congenital unilateral absence of a pulmonary artery.Am J Cardiol 10:706–732
Rosenberg HS, Hallman GL, Wolfe RR, Latson JR (1966) Origin of the right pulmonary artery from the aorta.Am Heart J 72:106–115
Schneiderman LJ (1958) Isolated congenital absence of the right pulmonary artery: A caution as to its diagnosis and a proposal for its embryogenesis: Report of a case with review.Am Heart J 55:772–780
Wagenvoort CA, Neufeld HN, Birge RF, Caffrey JA, Edwards JE (1961) Origin of right pulmonary artery from ascending aorta.Circulation 23:84–90A0946012 00003 CS-SPJRNPDF [HEADSUP]
Author information
Authors and Affiliations
Rights and permissions
About this article
Cite this article
Pfefferkorn, J.R., Löser, H., Pech, G. et al. Absent pulmonary artery. Pediatr Cardiol 3, 283–286 (1982). https://doi.org/10.1007/BF02427028
Issue Date:
DOI: https://doi.org/10.1007/BF02427028