Summary
Diagnosis and successful surgical repair of cor triatriatum, associated with anomalous pulmonary/systemic venous connection in a 6-month-old infant, is described. Follow-up at 2 years revealed no abnormalities.
The clinical findings, hemodynamics, and surgical treatment are discussed, together with a review of the literature. This is a rare, life-threatening situation presenting significant diagnostic difficulties in infancy. It is, however, amenable to surgery provided that an early diagnosis is achieved.
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Hess, J., Brenken, U., Eygelaar, A. et al. Successful management of cor triatriatum associated with anomalous pulmonary/systemic venous connection in an infant. Pediatr Cardiol 2, 319–322 (1982). https://doi.org/10.1007/BF02426981
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DOI: https://doi.org/10.1007/BF02426981