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Congenital heart disease in the Pierre Robin syndrome

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Summary

Congenital heart disease occurs in about 20 percent of patients with Pierre Robin syndrome. Ventricular septal defect, patent ductus arteriosus, and atrial septal defect are the most common congenital cardiac lesions in this syndrome. The associated upper airway obstruction can produce cor pulmonale, cardiomegaly, pulmonary edema, and cyanosis.

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Authors and Affiliations

  1. Division of Pediatric Cardiology, William Beaumont Army Medical Center, Box 70614, El Paso, Texas, 79920

    William Pearl M.D.

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  1. William Pearl M.D.
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Pearl, W. Congenital heart disease in the Pierre Robin syndrome. Pediatr Cardiol 2, 307–309 (1982). https://doi.org/10.1007/BF02426978

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  • DOI: https://doi.org/10.1007/BF02426978

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