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Scimitar syndrome in neonates: Report of four cases and review of the literature

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Summary

Four neonates with scimitar syndrome are presented. Three of the cases had congenital cardiovascular abnormalities not usually regarded as part of the scimitar syndrome, namely, ventricular septal defect, abnormalities of the aortic arch, and abnormal relationship of the pulmonary arteries and bronchi. Review of the literature indicates that among subjects of all ages the incidence of additional congenital heart disease is 24%; in patients within the pediatric age group the incidence is about 36% and is highest (75%) among those subjects having diagnostic studies while neonates.

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Authors and Affiliations

  1. Department of Pathology, United Hospitals, St. Paul

    Daniel K. Gikonyo, Rajendra Tandon, Russell V. Lucas Jr. & Jesse E. Edwards

  2. Department of Pathology, University of Minnesota, Minneapolis, Minnesota, USA

    Daniel K. Gikonyo, Rajendra Tandon, Russell V. Lucas Jr. & Jesse E. Edwards

  3. Department of Pediatric Cardiology, University of Minnesota, Minneapolis, Minnesota, USA

    Daniel K. Gikonyo, Rajendra Tandon, Russell V. Lucas Jr. & Jesse E. Edwards

  4. Department of Pediatric Cardiology, All India Institute of Medical Science, New Delhi, India

    Daniel K. Gikonyo, Rajendra Tandon, Russell V. Lucas Jr. & Jesse E. Edwards

Authors
  1. Daniel K. Gikonyo
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  2. Rajendra Tandon
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  3. Russell V. Lucas Jr.
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  4. Jesse E. Edwards
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Additional information

This study was supported by the Saint Paul Foundation, Parents-For-Heart, the Minnesota Medical Foundation, and the Dwan Family Fund.

Supported by the Department of Medicine, University of Nairobi, Kenya.

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Gikonyo, D.K., Tandon, R., Lucas, R.V. et al. Scimitar syndrome in neonates: Report of four cases and review of the literature. Pediatr Cardiol 6, 193–197 (1986). https://doi.org/10.1007/BF02310997

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