Summary
A 17-year-old girl with Cogan's syndrome is described. Total and irreversible hearing loss occurred which was unresponsive to corticosteroids and immunosuppressive therapy. The girl died a year later from subarachnoid haemorrhage. The lethal prognosis in Cogan's syndrome despite the available treatment is emphasized.
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Vaiopoulos, G., Sfikakis, P.P., Skoumas, B. et al. Lack of response to corticosteroids and pulse cyclophosphamide therapy in Cogan's syndrome. Clin Rheumatol 13, 110–112 (1994). https://doi.org/10.1007/BF02229876
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DOI: https://doi.org/10.1007/BF02229876