Abstract
The Rapunzel syndrome (RS), is a rare form of gastric trichobezoar extending throughout the bowel. We report on a patient with RS causing gastric perforation and discuss the aetiology, pathogenesis, diagnosis and treatment of this unusual syndrome. RS is found characteristically in girls with varying gastro-intestinal symptoms. The recommended treatment for large or complicated trichobezoars is surgery. Psychiatric follow up is essential to diminish the frequency of reccurrence.
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References
Andrus CH, Ponsky JL (1988) Bezoars: classification, pathophysiology and treatment. Am J Gastroenterol 83: 476–478
Avissar E, Goldberg M, Lernau O (1994) Bezoar-induced ulceration and perforation of the upper gastrointestinal tract in mentally retarded patients. Pediatr Surg Int 9: 279–280
Balik E, Ulman I, Taneli C, Demircan M (1993) The Rapunzel syndrome: a case report and review of the literature. Eur J Pediatr Surg 3: 171–173
De Bakey M, Ochsner A (1938) Bezoars and concreations, comprehensive review of literature with analysis 303 collected cases and presentation of 8 additional cases. Surgery 4: 934–963
Deslypere JP, Pract M, Verdonk G (1982) An unusual case of trichobezoar: the Rapunzel syndrome. Am J Gastroenterol 77: 467–470
Pandeya NK (1973) Trichobezoar: case presentation and review of literature. J Am Osteopathol Assoc 72: 628–634
Vaughan ED, Sawyers JL, Scott HW (1968) The Rapunzel syndrome: an unusual complication of intestinal bezoar. Surgery 63: 339–343
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Pul, N., Pul, M. The rapunzel syndrome (trichobezoar) causing gastric perforation in a child: A case report. Eur J Pediatr 155, 18–19 (1996). https://doi.org/10.1007/BF02115620
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DOI: https://doi.org/10.1007/BF02115620