Summary
Two children suffering from systemic juvenile chronic arthritis (JCA)11 complicated by acute disseminated intravascular coagulation (DIG) are described. One had a fatal outcome with acute renal failure and cerebral haemorrhage; the other recovered. Early recognition and treatment of the underlying cause — usually an infection — as well as replacement of clotting factors are important in management.
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De Vere-Tyndall, A., Macauley, D. & Ansell, B.M. Disseminated intravascular coagulation complicating systemic juvenile chronic arthritis (”Still's disease”). Clin Rheumatol 2, 415–418 (1983). https://doi.org/10.1007/BF02041564
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DOI: https://doi.org/10.1007/BF02041564