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Posttraumatic hepatic vein thrombosis (Budd-Chiari syndrome) in a child

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Abstract

The Budd-Chiari syndrome (BCS) results from hepatic venous outflow obstruction and is characterized by massive ascites and painful hepatomegaly. It is a rare condition, particularly in children, and is often fatal without surgical intervention. Although several conditions resulting in a hypercoagulable state appear to predispose individuals to developing the disorder in adulthood, the etiology in children is often obscure. We present the case of a 6-year-old girl treated nonoperatively for blunt abdominal trauma and hemoperitoneum. Two weeks following her injury, she developed an acute BCS with rapid liver failure, ascites, and abdominal pain. The diagnosis of hepatic vein thrombosis was confirmed radiographically and the patient underwent a C-type mesocaval shunt procedure. The etiology, diagnosis, and surgical management of BCS in children and a review of the literature are discussed.

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Authors and Affiliations

  1. Division of Pediatric Surgery, Department of Surgery, The Johns Hopkins University School of Medicine, Baltimore, Maryland, USA

    Peter Mattei & Paul M. Colombani

  2. Division of Pediatric Radiology, Department of Radiology, The Johns Hopkins University School of Medicine, Baltimore, Maryland, USA

    George A. Taylor

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  1. Peter Mattei
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  2. George A. Taylor
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  3. Paul M. Colombani
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Mattei, P., Taylor, G.A. & Colombani, P.M. Posttraumatic hepatic vein thrombosis (Budd-Chiari syndrome) in a child. Pediatr Surg Int 9, 425–428 (1994). https://doi.org/10.1007/BF01686026

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  • DOI: https://doi.org/10.1007/BF01686026

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