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Coarctation of the aorta and renal artery stenosis in tuberous sclerosis

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Abstract

Among neurocutaneous disorders, coarctation of the abdominal aorta and renal artery stenosis have traditionally been associated with neurofibromatosis. We report a 5-year-old girl who, during the evaluation of asymptomatic hypertension, was discovered to have bilateral renal artery stenosis, coarctation of the abdominal aorta, renal cysts and typical skin lesions of tuberous clerosis. Renal vascular hypertension has not been reported previously in tuberous sclerosis. We conclude that the tuberous sclerosis complex should be expanded to include vascular malformations and that hypertension should not be assumed to be secondary to renal hamartomata or cysts in patients with tuberous sclerosis.

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Authors and Affiliations

  1. Departments of Pediatrics, Pathology and Radiology, University of Tennessee Center for the Health Sciences and LeBonheur Children's Medical Center, Memphis, Tennessee, USA

    P. M. Flynn, M. B. Robinson, F. B. Stapleton, S. Roy Jr., G. Koh & I. L. D. Tonkin

  2. Pediatric Research Laboratory, 956 Court Avenue, Room 3B09, 38163, Memphis, Tennessee, USA

    F. B. Stapleton

Authors
  1. P. M. Flynn
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  2. M. B. Robinson
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  3. F. B. Stapleton
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  4. S. Roy Jr.
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  5. G. Koh
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  6. I. L. D. Tonkin
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Flynn, P.M., Robinson, M.B., Stapleton, F.B. et al. Coarctation of the aorta and renal artery stenosis in tuberous sclerosis. Pediatr Radiol 14, 337–339 (1984). https://doi.org/10.1007/BF01601889

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  • DOI: https://doi.org/10.1007/BF01601889

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