Abstract
A case of primary signet-ring-cell carcinoma of the rectum is presented. Colorectal carcinoma is uncommon in childhood; moreover, the signet-ring-cell type is very rare even in adults. The clinical, pathologic, and biologic characteristics of this carcinoma are different from ordinary colorectal carcinomas. Our patient was a 12-year-old boy, the youngest with a signet-ring-cell carcinoma of the rectum in the English literature, who had a Dukes' C lesion. Pathologically, the tumor is characterized by diffuse infiltration of the bowel wall by signet-ring-cells. The prognosis is extremely poor.
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Yoo, SY., Lee, JH., Park, KR. et al. Primary signet-ring-cell carcinoma of the rectum in a 12-year-old boy. Pediatr Surg Int 9, 284–286 (1994). https://doi.org/10.1007/BF00832259
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DOI: https://doi.org/10.1007/BF00832259