Abstract
Congenital central alveolar hypoventilation (C-CAH), so called Ondine's curse, is known to be quite a rare neuropathology that has been reported in only 23 cases to date. C-CAH was diagnosed in a 2-year-5-month-old infant. In the treatment of C-CAH, we implanted a right unilateral diaphragm pacemaker in the infant and his respiratory status was remarkably improved after diaphragm pacing. Twenty-three reported cases of this disorder are reviewed in the literature.
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Abbreviations
- C-CAH:
-
congenital central alveolar hypoventilation
- IPPV:
-
intermittent positive pressure ventilation
- DP:
-
diaphragm pacing
References
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Yasuma, F., Nomura, H., Sotobata, I. et al. Congenital central alveolar hypoventilation (Ondine's curse): a case report and review of the literature. Eur J Pediatr 146, 81–83 (1987). https://doi.org/10.1007/BF00647295
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DOI: https://doi.org/10.1007/BF00647295