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Zur Pathologie und Genese des extramammären Morbus Paget

On pathology and genesis of the extramammary Paget's disease

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Summary

In a compilation of the secured observations of extramammary Morbus Paget the age of manifestation, the duration and the relation of male and female cases are investigated. The common image of the disease and one observation of a case of perianal extramammary Paget's disease are described. The various opinions of the nature and genesis of the Paget-carcinoma set forth in literature are discussed on the basis of histological studies. The term „adenocarcinoma apocrinocellulare epidermotropicum” is suggested as the definition of the disease.

Zusammenfassung

In einer Zusammenstellung der gesicherten Beobachtungen von extramammärem Morbus Paget wird das Manifestationsalter, die Verlaufsdauer und die Verteilung der Erkrankung auf die Geschlechter ermittelt. Das klassische Bild der Erkrankung und eine eigene Beobachtung eines Falles von perianaler extramammärer Pagetscher Erkrankung werden beschrieben. Zu den verschiedenen Ansichten über die Natur und die Genese des Paget-Carcinoms im Schrifttum wird an Hand von histologischen Studien Stellung genommen und die Definition der Erkrankung als „Adenocarcinoma apocrinocellulare epidermotropicum” vorgeschlagen.

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    G. Lüders

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Lüders, G. Zur Pathologie und Genese des extramammären Morbus Paget. Arch. klin. exp. Derm. 232, 16–32 (1968). https://doi.org/10.1007/BF00522752

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