Abstract
Bilateral radiographic irregularities and deformities of the proximal femoral epiphyses are features of both multiple epiphyseal dysplasia and bilateral idiopathic avascular necrosis. In the past these entities have been difficult to differentiate. This report documents radiographically the occurrence of avascular necrosis in 10 patients with multiple epiphyseal dysplasia by recognizing the superimposition of sclerosis and subchondral fissuring on pre-existing symmetrically irregular proximal femoral ossification centers. Scintigraphic (photopenia) or magnetic resonance (loss of signal) criteria of avascular necrosis confirm its added presence and help to establish an imaging scheme to identify avascular necrosis superimposed on multiple epiphyseal dysplasia.
Similar content being viewed by others
References
Crossan, JF, Wynne-Davies R, Folford GE (1983) Bilateral failure of capital femoral epiphysis, bilateral Perthes' disease, multiple epiphyseal dysplasia, pseudoachondroplasia, and spondyloepiphyseal dysplasia. J Pediatr Orthop 3:297
Egund N, Wingstrand H, Forsberg L, Petterson H, Sunden G (1986) Computed tomography, and ultrasonography for diagnosis of hip joint effusion in children. Acta Orthop Scand 57:211
Gelfand MJ, Ball WS, Oestreich AE, Crawford AL, Jolson R, Perlman A (1983) Transient loss of femoral head Tc-99m diphosphonate uptake with a prolonged maintenance of femoral head architecture. Clin Nucl Med 8:347
Griffiths HED, Witherow PJ (1977) Perthes' disease and multiple epiphyseal dysplasia. Postgrad Med J 53:464
Kloiber R, Pavlosky W, Portner O, Gartke K (1983) Bone scintigraphy of hip joint effusions in children. AJR 140995
Mandell GA, Harcke HT, Bowen JR Sharkey CA (1989) Reversible ischemia following arthrography. Clin Nucl Med (in press)
Meyer J (1964) Dysplasia epiphysealis capitis femoris. A clinical-radiological syndrome and its relationship to Legg-Calve-Perthes' disease. Acta Orthop Scand 34:183
Ozonoff MB (1979) Pediatric orthopedic radiology. WB Saunders, Philadelphia, p 155
Schlesinger AE, Poznanski AK, Pudlowski RM, Millar EA (1986) Distal femoral epiphysis: Normal standards for thickness and application to bone dysplasias. Radiology 159:515
Scoles PV, Yoon YS, Makley JT, Kalamchi A (1984) Nuclear magnetic resonance imaging in Legg-Calve-Perthes' disease. J Bone Joint Surg [Am] 66:1357
Shephard E (1956) Multiple epiphyseal dysplasia. J Bone Joint Surg [Br] 38:458
Stephens FE, Kerby JP (1946) Hereditary Legg-Calve-Perthes' disease. J Hered 37:153
Toby EB, Koman LA, Bechtold RE (1985) Magnetic resonance imaging of pediatric hip disease. J Pediatr Orthop 5:665
Traughber PD, Manaster BJ, Murphy K, Alazraki NP (1986) Negative bone scans of joints after aspiration or arthrography: Experimental studies. AJR 146:87
Wingstrand H, Egrund N, Carlin NO, Forsberg L, Gustafson T, Sunden G (1985) Intracapsular pressure in transient synovitis of the hips. Acta Orthop Scand 56:204
Author information
Authors and Affiliations
Rights and permissions
About this article
Cite this article
Mandell, G.A., MacKenzie, W.G., Scott, C.I. et al. Identification of avascular necrosis in the dysplastic proximal femoral epiphysis. Skeletal Radiol 18, 273–281 (1989). https://doi.org/10.1007/BF00361206
Issue Date:
DOI: https://doi.org/10.1007/BF00361206