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Opsoclonus-myoclonus syndrome: correlation of radiographic and pathological observations

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Summary

We report a case of a child with opsoclonus-myoclonus syndrome. Neuroradiological studies indicated a lesion in the cerebellar vermis. A cerebellar biopsy revealed changes consisting of Purkinje and granular cell loss with gliosis. This case report documents the correlation of radiologic and pathological findings in a patient with opsoclonus-myoclonus syndrome.

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Authors and Affiliations

  1. Department of Neurology, Albert Einstein College of Medicine, Bronx, New York, USA

    R. F. Tuchman, L. A. Alvarez & S. L. Moshe

  2. Department of Neurosurgery, Albert Einstein College of Medicine, Bronx, New York, USA

    A. B. Kantrowitz

  3. Department of Neuroradiology, Albert Einstein College of Medicine, Bronx, New York, USA

    F. G. Moser

  4. Department of Neuropathology, Albert Einstein College of Medicine, Bronx, New York, USA

    J. Llena

  5. Department of Pediatrics, Albert Einstein College of Medicine, Bronx, New York, USA

    S. L. Moshe

  6. Montefiore Medical Center, Bronx, New York, USA

    S. L. Moshe

  7. Department of EEG, Montefiore Medical Center-NW3, 111 East 210th Street, 10467, Bronx, NY, USA

    R. F. Tuchman

Authors
  1. R. F. Tuchman
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  2. L. A. Alvarez
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  3. A. B. Kantrowitz
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  4. F. G. Moser
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  5. J. Llena
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  6. S. L. Moshe
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Tuchman, R.F., Alvarez, L.A., Kantrowitz, A.B. et al. Opsoclonus-myoclonus syndrome: correlation of radiographic and pathological observations. Neuroradiology 31, 250–252 (1989). https://doi.org/10.1007/BF00344353

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  • DOI: https://doi.org/10.1007/BF00344353

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