Abstract
Thirteen patients with symptomatic polycystic liver disease who were selected for fenestration were reviewed. The main preoperative complaints that related to polycystic liver disease were severe abdominal pain, respiratory distress, clinical ascites, or leg edema. All symptoms disappeared after operation, and the number and size of the cysts were smaller. Five patients developed transient but massive ascites during the postoperative period, and long-term follow-up demonstrated a moderate recurrence of hepatomegaly in two patients. These postoperative complications and failures appeared to be at least partly related to a more extensive evolution of the disease in the patients in whom it developed.
Résumé
Treize patients ayant une maladie polykystique du foie et sélectionnés pour fénestration ont été analysés. Les plaintes habituelles ont été essentiellement la doulcur abdominale sévère, une gène respiratoire, une ascite clinique ou de l'oedème des membres inférieurs. Tous ces symptômes ont disparu après opération et le nombre et la taille de ces kystes étaient plus petits. Cinq patients ont développé une ascite massive en période postopératoire et le suivi à distance a démontré une récidive de l'hépatomégalie chez deux patients. Ces complications postopératoires et les échecs sont probablement, du moins en partie, en rapport avec une plus grande évolutivité chez les patients atteints.
Resumen
Se revisaron 13 pacientes con enfermedad poliquística del hígado que habían sido seleccionados para fenestración. Los principales síntomas relacionados con la enfermedad poliquística del hígado fueron dolor abdominal severo, dificultad respiratoria, ascitis clínica o edema de las extremidades inferiores. Todos los síntomas desaparecieron luego de la operación y el número y tamaño de los quistes disminuyeron. Cinco pacientes desarrollaron ascitis transitoria pero masiva en el período postoperatorio y el seguimiento a largo plazo demostró moderada recurrencia de la hepatomegalia en dos pacientes. Estas complicaciones aparecieron relacionadas, por lo menos en parte, con una mayor capacidad de evolución de la enfermedad.
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Farges, O., Bismuth, H. Fenestration in the management of polycystic liver disease. World J. Surg. 19, 25–30 (1995). https://doi.org/10.1007/BF00316975
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DOI: https://doi.org/10.1007/BF00316975