Summary
Two patients with chorea and polycythaemia vera are described. The literature on this rare association is reviewed and its pathophysiology discussed.
Similar content being viewed by others
References
Alajouanine Th, Boudin G, André R, Goudal H (1952) Les manifestations nerveuses de la maladie de Vaquez. Bull Mem Soc Med Hôp Paris 68:538–549
Ashenhurst EM (1972) Chorea complicating polycythaemia rubra vera. Can Med Assoc J 107:434–437
Bakke JV, Staven J (1963) Chorea and polycythaemia. Nord Med 63:200–202
Bardachzi F (1909) Polyzythämie mit Chorea. Prag Med Wochenschr 34:253–255
Bietti C, Pompili A, Sinibaldi L (1968) Coreoatetosi in malattia di Vaquez. Riv Neurol 38:615–626
Borg-Costanzi JM, Mohr PD, Lewis D (1981) Primary polycythaemia presenting with chorea. Postgrad Med J 57:228–231
Bruyn GW, Padberg G (1984) Chorea and polycythaemia. Eur Neurol 23:26–33
Edwards PD, Prosser R, Wells CEC (1975) Chorea, polycythaemia, and cyanotic heart disease. J Neurol Neurosurg Psychiatry 39:729–739
Friedemann M, Mumenthaler M, Kummer H (1965) Chorea bei polycythaemia vera. Dtsch Z Nervenheilkd 187:585–594
Gauthier-Smith PC, Prankerd TAJ (1967) Polycythaemia vera and chorea. Acta Neurol Scand 43:357–364
Harvier P, Laffitte A, Lavarenne G (1950) Maladie de Vaquez et chorée. Paris Med 20:277–282
Heathfield KWG (1968) Polycythaemia and chorea. Br Med J 1:250
Hutchinson R, Miller CH (1906) A case of splenomegalic polycytaemia with report of post-mortem examination. Lancet I:744–746
Kotner LM, Tritt JH (1942) Chorea complicating polycythaemia vera; report of a case. Ann Intern Med 17:544–548
Modan B (1965) An epidemiological study of polycythaemia vera. Blood 26:657–667
Monteverde A, de Sasot S, de Bernardou EM (1983) _ Corea policitemica. Rev Neurol Arg 9:3–8
Morre HHE, van Woerkom TCAM, Endtz LJ (1982) A case of chorea due to polycythaemia vera. Clin Neurol Neurosurg 84:125–130
Naville F, Brütsch P (1919) Les complications cérébrales et médullaires de la maladie de Vaquez (Erythrémie). Schweiz Arch Neurol Psychiatr 4:88–103
Paliard F, Croizat P, Schott B (1958) Choréo-athétose récidivante révélatrice de maladie de Vaquez. Lyon Med 200:353–362
Pollock LJ (1922) A case of chorea and erythremia. JAMA 78:724–726
Sangster JF (1970) Polycythaemia vera and chorea. Australas Ann Med 4:354–357
Schiff P, Trelles JO, Ajuriaguerra J (1936) Sur un syndrome particulier d'origine pallidale. Erythrémie avec chorée. Encéphale 31:153–173
Silverstein A, Gilberg H, Wassermann LR (1962) Neurologic complications of polycythaemia. Ann Intern Med 57:909–916
Van Trotsenburg L, Koster M (1954) Chorea caused by polycythaemia vera and treated with radioactive phosphorus. Folia Psychiatr Neurol Neurochir Neerl 57:420–434
Voiculescu V, Ionescu DA, Lazar G, Alecu C, Predescu C, Popa C, Xenakis A, Marcu I, Ghitescu M (1979) Two cases of choreatic syndrome caused by polycythaemia vera. Eur Neurol 18:96–100
Wade JPH (1983) Transport of oxygen to the brain in patients with elevated haematocrit values before and after venesection. Brain 106:513–523
Wetherley-Mein G, Pearson TC (1982) The myeloproliferative disorders. In: Hardisty RM, Weatherall DJ (eds) Blood and its disorders. Blackwell Scientific Publications, Oxford
Yiannikas C, McLeod JG, Walsh JC (1983) Peripheral neuropathy associated with polycythemia vera. Neurology 33:139–143
Author information
Authors and Affiliations
Rights and permissions
About this article
Cite this article
Mas, J.L., Gueguen, B., Bouche, P. et al. Chorea and polycythaemia. J Neurol 232, 169–171 (1985). https://doi.org/10.1007/BF00313895
Received:
Accepted:
Issue Date:
DOI: https://doi.org/10.1007/BF00313895