Summary
The clinicopathological findings of a 58-year-old man, who developed cervicothoracic syringomyelia at the age of 25 are presented. He was given radiation therapy at the age of 33. At the age of 57 he developed a foramen jugulare syndrome on the left, caused by a low grade leiomyosarcoma. Etiologically, the most attractive hypothesis appears to be that the tumour was induced by radiation therapy administered 24 years previously.
Zusammenfassung
Es werden die klinischen sowie pathologisch-anatomischen Befunde bei einem 58jährigen Patienten beschrieben, der im Alter von 25 Jahren die ersten Symptome einer zervikothorakalen Syringomyelie entwickelte und im Alter von 33 Jahren röntgenbestrahlt wurde. Mit 57 Jahren trat ein Foramen-jugulare-Syndrome links in Erscheinung, welches auf ein sanduhrförmiges Leiomyosarkom zurückzuführen war. Es scheint am wahrscheinlichsten, daß dieser Tumor durch die 24 Jahre früher durchgeführte Bestrahlung der Nackenregion induziert wurde.
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Sieben, G., Sieben-Praet, M., De Reuck, J. et al. Dumb-bell sarcoma of the foramen jugulare with syringomyelia. A radio-induced tumour?. J Neurol 222, 219–225 (1980). https://doi.org/10.1007/BF00313150
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DOI: https://doi.org/10.1007/BF00313150