Abstract
A restospective study was performed on all babies presenting to Princess Mary Hospital, Auckland, with conjugated hyperbilirubinaemia. Twenty-six were diagnosed as having biliary atresia. Of these, 7 (27%) are excreting bile and remain jaundice free, 1 remains jaundiced but is still alive, and the remainder (69%) have died of terminal liver failure. Seven babies had associated anomalies. The incidence in Polynesians was 10 times higher than that in Caucasians. Ultrasound plus DISIDA scan was extremely sensitive at diagnosing the condition. Cholangitis remains the major postoperative problem, affecting all excretors.
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Schroeder, D., Pease, P.W.B. Biliary atresia A review of the Auckland experience. Pediatr Surg Int 4, 101–104 (1989). https://doi.org/10.1007/BF00181843
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DOI: https://doi.org/10.1007/BF00181843