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A Classification of Renal Cysts

  • Chapter
The Cystic Kidney

Part of the book series: Developments in Nephrology ((DINE,volume 27))

Abstract

Renal cystic diseases are a mixed lot, comprising heritable, developmental and acquired disorders. This classification has been developed, as have several others in the past, to incorporate radiographic, functional and genetic information, and to provide a basis for clinicopathologic correlations. Its major categories are as follows: (1) polycystic kidney diseases, autosomal recessive and autosomal dominant; (2) renal cysts in hereditary syndromes, including tuberous sclerosis, orofaciodigital syndrome and von Hippel-Lin- dau disease; (3) glomerulocystic kidney disease, a descriptive category of considerable heterogeneity; (4) localized segmental and unilateral renal cysts, and solitary and simple renal cysts; (5) acquired cystic disease, usually resulting in end-stage kidneys; (6) medullary cysts, occurring both as medullary sponge kidney and as an accompaniment of hereditary tubulointerstitial nephritis; (7) renal dysplasia, including multicystic dysplasia and diffuse cystic dysplasia; and (8) extraparenchymal cysts. This classification has remained essentially unchanged for more than a decade and has served its purposes satisfactorily.

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  1. J. Bernstein
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Editors and Affiliations

  1. Department of Medicine, University of New Mexico Hospital, Albuquerque, USA

    Kenneth D. Gardner Jr.

  2. Department of Anatomic Pathology, William Beaumont Hospital, Royal Oak, USA

    Jay Bernstein

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© 1990 Kluwer Academic Publishers

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Bernstein, J. (1990). A Classification of Renal Cysts. In: Gardner, K.D., Bernstein, J. (eds) The Cystic Kidney. Developments in Nephrology, vol 27. Springer, Dordrecht. https://doi.org/10.1007/978-94-009-0457-6_7

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  • DOI: https://doi.org/10.1007/978-94-009-0457-6_7

  • Publisher Name: Springer, Dordrecht

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  • Online ISBN: 978-94-009-0457-6

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