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Treatment of Lymphatic Malformations

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Hemangiomas and Vascular Malformations

Abstract

The development of the Hamburg Classification, along with a better understanding of vascular malformations, has allowed a more concise description of lymphatic malformation (LM). The management of LM has become clear: “lymphangioma” shou no longer be considered a single LM lesion, but rather one of two different LM lesions belonging to an extratruncular lesion, even though the management of lymphangioma is different from its “truncular” lesion counterpart that clinically presents as primary lymphedema. Although they often present as discrete clinical entities, the lesions can occur together, making clinical management confusing.

Treatment options for lymphangioma should be approached cautiously with appropriate consideration of its embryologic characteristics, as for any other extratruncular lesion, when options such as sclerotherapy and/or surgical excision are being considered.

Primary lymphedema should be managed as a truncular lesion, where decongestive physiotherapy remains the mainstay of treatment to improve lymph-transporting function. Additional surgical therapy, either reconstructive or ablative, should only be carried out as a supplemental therapy with justifiable indications.

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Author information

Authors and Affiliations

  1. Center for Vein, Lymphatics and Vascular Malformation, Division of Vascular Surgery, Georgetown University School of Medicine, Washington, DC, USA

    Byung-Boong Lee

  2. Department of Surgery Division of Vascular Surgery, Georgetown University Hospital, Washington, DC, USA

    James Laredo & Richard F. Neville

  3. Division of Pediatric Surgery, SamSung Medical Center & Sungkyunkwan University, Kangnam-Ku, Seoul, Korea

    Jeong-Meen Seo

Authors
  1. Byung-Boong Lee
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  2. James Laredo
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  3. Jeong-Meen Seo
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  4. Richard F. Neville
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Editor information

Editors and Affiliations

  1. Department of Vascular Surgery, Center for Vascular Malformations “Stefan Belov”, “G. Salvini” Hospital, Garbagnate Milanese (Milan), Italy

    Raul Mattassi  & Massimo Vaghi  & 

  2. Center for Circulatory Disturbances and Vascular Defects, Department for Angiology and Vascular Surgery, Facharztklinik Hamburg, Hamburg, Germany

    Dirk A. Loose

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Lee, BB., Laredo, J., Seo, JM., Neville, R.F. (2009). Treatment of Lymphatic Malformations. In: Mattassi, R., Loose, D.A., Vaghi, M. (eds) Hemangiomas and Vascular Malformations. Springer, Milano. https://doi.org/10.1007/978-88-470-0569-3_29

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  • DOI: https://doi.org/10.1007/978-88-470-0569-3_29

  • Publisher Name: Springer, Milano

  • Print ISBN: 978-88-470-0568-6

  • Online ISBN: 978-88-470-0569-3

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