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Risk Stratification and Antiarrhythmic Drug Therapy

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Arrhythmogenic RV Cardiomyopathy/Dysplasia

Abstract

Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is an important cause of ventricular tachyarrhythmias and sudden death in young patients and athletes with apparently normal hearts. The disease is characterized by localized or diffuse atrophy of predominantly right ventricular myocardium with subsequent replacement by fatty and fibrous tissue. As a result of these pathomorphological alterations, global and regional right (and left) ventricular dysfunction and ventricular tachyarrhythmias due to areas of slow conduction and dispersion of refractoriness are the major clinical findings and manifestations of ARVC/D [1–4].

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Author information

Authors and Affiliations

  1. Department of Cardiology and Angiology, University Hospital of Münster, Münster, Germany

    Thomas Wichter MD, FESC & Matthias Paul MD

  2. Department of Cardiological, Thoracic and Vascular Sciences, University of Padua, Italy

    Domenico Corrado MD, PhD

Authors
  1. Thomas Wichter MD, FESC
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  2. Domenico Corrado MD, PhD
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  3. Matthias Paul MD
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Editor information

Editors and Affiliations

  1. Section of Cardiology, Department of Medicine, Sarver Heart Center, University of Arizona, Tucson, AZ, USA

    Frank I. Markus

  2. Department of Cardiological, Thoracic and Vascular Sciences, University of Padua, Italy

    Andrea Nava

  3. Department of Medical Diagnostic Sciences, University of Padua, Italy

    Gaetano Thiene

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© 2007 Springer-Verlag Italia

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Wichter, T., Corrado, D., Paul, M. (2007). Risk Stratification and Antiarrhythmic Drug Therapy. In: Markus, F.I., Nava, A., Thiene, G. (eds) Arrhythmogenic RV Cardiomyopathy/Dysplasia. Springer, Milano. https://doi.org/10.1007/978-88-470-0490-0_19

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  • DOI: https://doi.org/10.1007/978-88-470-0490-0_19

  • Publisher Name: Springer, Milano

  • Print ISBN: 978-88-470-0489-4

  • Online ISBN: 978-88-470-0490-0

  • eBook Packages: MedicineMedicine (R0)

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