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Aggressive Fibromatosis

Extra-Abdominal Desmoid Tumor, Musculo-Aponeurotic Fibromatosis

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Bone and Soft Tissue Tumors

Abstract

Aggressive fibromatosis is a slow growing, permeative tumor, uniformly composed of fibroblasts-fibrocytes and abundant collagen, and located in the deep soft tissues. Despite the fact that aggressive fibromatosis behaves similarly to a low-grade sarcoma, it is kept separate from fibrosarcoma. Nonetheless, the limit of distinction with grade 1 fibrosarcoma is sometimes unclear and difficult to determine.

Desmoid tumor of the abdominal wall mostly occurs in females during pregnancy or after delivery.

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Author information

Authors and Affiliations

  1. University of Bologna, Italy

    Mario Campanacci M.D. (Orthopaedic Surgeon, Professor of Orthopaedic Surgery and Pathology, Director of the 1st Orthopaedic Clinic, Director of the Graduate School of Orthopaedics, Director of the Tumor Centre)

  2. Rizzoli Orthopaedic Institute, Bologna, Italy

    Mario Campanacci M.D. (Orthopaedic Surgeon, Professor of Orthopaedic Surgery and Pathology, Director of the 1st Orthopaedic Clinic, Director of the Graduate School of Orthopaedics, Director of the Tumor Centre)

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  1. Mario Campanacci M.D.
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© 1999 Springer-Verlag Wien

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Campanacci, M. (1999). Aggressive Fibromatosis. In: Bone and Soft Tissue Tumors. Springer, Vienna. https://doi.org/10.1007/978-3-7091-3846-5_61

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  • DOI: https://doi.org/10.1007/978-3-7091-3846-5_61

  • Publisher Name: Springer, Vienna

  • Print ISBN: 978-3-7091-3848-9

  • Online ISBN: 978-3-7091-3846-5

  • eBook Packages: Springer Book Archive

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