Abstract
The incidence of sudden death in hypertrophic cardiomyopathy is approximately 2%–4% per year in adults and 4%–6% per year in children and adolescents [1]. These data have been generated from referral cardiac centres and may reflect a bias to the more severe patients [2]. The changes in diagnostic criteria and widespread use of more sensitive diagnostic techniques (two-dimensional echocardiography) have not resulted in a significantly different incidence of sudden death. The annual mortality in children followed at the Hammersmith Hospital who were essentially asymptomatic and did not have a family history of sudden death was 3.5%–4% in the 1960s and 1970s and has not changed in the 1980s [3, 4]. The identification and management of patients with hypertrophic cardiomyopathy who are at increased risk of sudden death remains a major problem particularly in younger patients.
Article Note
Adapted from: McKenna WJ, Camm AJ (1989) Sudden death in hypertrophic cardiomyopathy. Assessment of patients at high risk. Circulation 80:1489–92.
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McKenna, W.J., Counihan, P.J., Chikamori, T. (1990). Sudden Death in Hypertrophic Cardiomyopathy: Identification and Management of High Risk Patients. In: Baroldi, G., Camerini, F., Goodwin, J.F. (eds) Advances in Cardiomyopathies. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-83760-9_8
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