Skip to main content

Anatomoclinical Aspects of Arrhythmogenic Right Ventricular Cardiomyopathy

  • Conference paper
Advances in Cardiomyopathies

Abstract

Cardiomyopathies are generally classified according to clinical and anatomic features, using an adjective to distinguish them. Thus, dilated (congestive) cardiomyopathy (DCM) indicates enlargement of the cardiac chambers with poor contractility and heart failure, hypertrophic cardiomyopathy implies hypertrophy of the ventricular septum in the setting of normal (or even increased) contractility, and restrictive cardiomyopathy denotes impaired compliance of the ventricles due to myocardial stiffness.

This is a preview of subscription content, log in via an institution to check access.

Access this chapter

Chapter
USD 29.95
Price excludes VAT (USA)
  • Available as PDF
  • Read on any device
  • Instant download
  • Own it forever
eBook
USD 39.99
Price excludes VAT (USA)
  • Available as PDF
  • Read on any device
  • Instant download
  • Own it forever
Softcover Book
USD 54.99
Price excludes VAT (USA)
  • Compact, lightweight edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info

Tax calculation will be finalised at checkout

Purchases are for personal use only

Institutional subscriptions

Preview

Unable to display preview. Download preview PDF.

Unable to display preview. Download preview PDF.

References

  1. Marcus FI, Fontaine GH, Guiraudon G, Frank R, Laurenceau JL, Malergue C, Grosgogeat Y (1982) Right ventricular dysplasia. A report of 24 adult cases. Circulation 65: 384–398

    Article  PubMed  CAS  Google Scholar 

  2. Virmani R, Rabinowitz M, Clark MA, Mc Allister HA (1982) Sudden death and partial absence of the right ventricular myocardium: a report of three cases and a review of the literature. Arch Pathol Lab Med 106: 163–163

    PubMed  CAS  Google Scholar 

  3. Froment R, Perrin A, Loire R, Dalloz C (1968) Ventricule droit papyrace’ du jeune adulte par dystrophie congénitale. A propos de 2 cas anatomocliniques et de 3 cas paracliniques. Arch Mal Coeur 61: 477–503

    PubMed  CAS  Google Scholar 

  4. Thiene G, Nava A, Corrado D, Rossi L, Pennelli N (1988) Right ventricular cardiomyopathy and sudden death in young people. N Engl J Med 318: 129–133

    Article  PubMed  CAS  Google Scholar 

  5. Nava A, Thiene G, Canciani B et al (1988) Familial occurrence of right ventricular dysplasia: A study involving nine families. J Am Coll Cardiol 12: 1222–1228

    Article  PubMed  CAS  Google Scholar 

  6. Perloff J (1988) Familial occurrence of right ventricular dysplasia: a study involving nine families (editorial). J Am Coll Cardiol 12:: 2229–1230

    Article  Google Scholar 

  7. Maron BJ (1988) Right ventricular cardiomyopathy: another cause of sudden death in the young. N Engl J Med 318: 178–180

    Article  PubMed  CAS  Google Scholar 

  8. Fontaine G, Frank R, Tonet JL et al (1984) Arrhythmogenic right ventricular dysplasia: a clinical model for the study of chronic ventricular tachycardia. Jpn Cire J 48: 515–538

    Article  CAS  Google Scholar 

  9. Nava A, Martini B, Thiene G, et al (1988) La displasia aritmogena del ventricolo destro. Studio su una popolazione selezionata. G Ital Cardiol 18: 2–9

    PubMed  CAS  Google Scholar 

  10. Nava A, Scognamiglio R, Thiene G, et al (1987) A polymorphic form of familial arrhythmogenic right ventricular dysplasia. Am J Cardiol 59: 1405–1409

    Article  PubMed  CAS  Google Scholar 

  11. Martini B, Nava A, Thiene G, et al (1988) Accelerated idioventricular rhythm of infundibular origin in patients with a concealed form of arrhythmogenic right ventricular dysplasia. Br Heart J 59: 564–571

    Article  PubMed  CAS  Google Scholar 

  12. Thiene G, Gambino A, Corrado D, Nava A (1986) The pathological spectrum underlying sudden death in athletes. New Trends Arrhythmias 1: 323–331

    Google Scholar 

  13. Nava A, Canciani B, Buja GF, Martini B, Daliento L, Scognamiglio R, Thiene G (1988) Electrovectorcardiographic study of negative T waves on precordial leads in arrhythmogenic right ventricular dysplasia: relationship with right ventricular volumes. J Electrocardiol 21: 239–245

    Article  PubMed  CAS  Google Scholar 

  14. Olsson SB, Edvardsson N, Emanuelsson H, Enestrom S (1982) A case of arrhythmogenic right ventricular dysplasia with ventricular fibrillation. Clin Cardiol 5: 591–594

    PubMed  CAS  Google Scholar 

  15. Manyari DE, Duff EJ, Kostuk WJ et al (1986) Usefulness of noninvasive studies for diagnosis of right ventricular dysplasia. Am J Cardiol 57: 1147–1153

    Article  PubMed  CAS  Google Scholar 

  16. Scognamiglio R, Fasoli G, Nava A, Buja GF (1987) Two-dimensional echocardiographic features in patients with spontaneous right ventricular tachycardia without apparent heart disease. J Cardiovasc Ultrason 6: 113–117

    Google Scholar 

  17. Scognamiglio R, Fasoli G, Nava A, Thiene G (1989) Relevance of subtle echocardiographic findings in the early diagnosis of the concealed form of right ventricular dysplasia. Eur Heart J 10: 59–64

    Google Scholar 

  18. Daubert C, Descaves C, Fulgoc JL, Bourdonnec C, Laurent M, Gouffault J (1988) Critical analysis of cineangiographic criteria for diagnosis of arrhythmogenic right ventricular dysplasia. Am Heart J 115: 448–459

    Article  PubMed  CAS  Google Scholar 

  19. Daliento L, Stritoni P, Isabella GB et al (1986) Malattia aritmogena primitiva del ventricolo destro: studio angiografico. Rev Lat Cardiol 7: 453–460

    Google Scholar 

  20. Thiene G, Angelini A, Valente M (1988) Biopsia endomiocardica nella cardiomiopatia aritmogena del ventricolo, destro. Cardiologia 33 (Suppl I) 313–315

    Google Scholar 

  21. Sugrue DD, Holmes DR, Gersh BJ et al (1984) Cardiac histologic findings in patients with life-threatening ventricular arrhythmias of unknown origin. J Am Coll Cardiol 4: 952–957

    Article  PubMed  CAS  Google Scholar 

  22. Morgera, Salvi A, Alberti E, Silvestri F, Camerini F (1985) Morphological findings in apparently idiopathic ventricular tachycardia. An echocardiographic, haemodynamic and histologic findings. Eur Heart J 6: 323–334

    PubMed  CAS  Google Scholar 

  23. Hasumi M, Sekiguki M, Hiroe M, Kasanuki H, Hirosawa K (1987) Endocardial biopsy approach to patients with ventricular tachycardia with special reference to arrhythmo-genic right ventricular dysplasia. Jpn Circ J 5: 242–249

    Article  Google Scholar 

  24. Blomstrom-Lundquist C, Sabel KG, Olsson SB 24 (1987) The long-term follow-up of 15 patients with arrhythmogenic right ventricular dysplasia. Br Heart J 58: 477–488

    Article  Google Scholar 

  25. Marshall WH, Furey M, Larsen B et al (1988) Right ventricular cardiomyopathy and sudden death in young people. N Engl J Med 319: 174 (Letter)

    Google Scholar 

  26. Waller BF, Smith ER, Blackbourne BD et al (1980) Congenital hypoplasia of portions of both right and left ventricular myocardial walls. Clinical and necropsy observations in two patients with parchment heart syndrome. Am J Cardiol 46: 885–891

    Article  PubMed  CAS  Google Scholar 

Download references

Authors

Editor information

Editors and Affiliations

Rights and permissions

Reprints and permissions

Copyright information

© 1990 Springer-Verlag Berlin Heidelberg

About this paper

Cite this paper

Thiene, G., Nava, A., Angelini, A., Daliento, L., Scognamiglio, R., Corrado, D. (1990). Anatomoclinical Aspects of Arrhythmogenic Right Ventricular Cardiomyopathy. In: Baroldi, G., Camerini, F., Goodwin, J.F. (eds) Advances in Cardiomyopathies. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-83760-9_41

Download citation

  • DOI: https://doi.org/10.1007/978-3-642-83760-9_41

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-642-83762-3

  • Online ISBN: 978-3-642-83760-9

  • eBook Packages: Springer Book Archive

Publish with us

Policies and ethics