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Epidermodysplasia Verruciformis: Immunological and Clinical Aspects

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Human Pathogenic Papillomaviruses

Part of the book series: Current Topics in Microbiology and Immunology ((CT MICROBIOLOGY,volume 186))

Abstract

Epidermodysplasia verruciformis (EV) is a rare life-long genetic skin disorder associated with specific human papillomaviruses (EV HPVs) and characterized by disseminated wart-like or pityriasis versicolor (PV)-like lesions and skin cancers. The cases may be familial or sporadic, and the inheritance is believed to be autosomal recessive (Lutzner 1978), although single cases of X-linked inheritance have been reported (Androphy et al. 1985).

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Authors and Affiliations

  1. Department of Dermatology, Warsaw School of Medicine, Koszykowa 82A, 02-008, Warsaw, Poland

    S. Jablonska & S. Majewski

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  1. S. Jablonska
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  2. S. Majewski
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  1. Deutsches Krebsforschungszentrum, Vorsitzender des Stiftungsrates, Im Neuenheimer Feld 280, D-69120, Heidelberg, Germany

    Harald zur Hausen

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Jablonska, S., Majewski, S. (1994). Epidermodysplasia Verruciformis: Immunological and Clinical Aspects. In: zur Hausen, H. (eds) Human Pathogenic Papillomaviruses. Current Topics in Microbiology and Immunology, vol 186. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-78487-3_9

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  • DOI: https://doi.org/10.1007/978-3-642-78487-3_9

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