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Bifid Scrotum

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Normal and Abnormal Scrotum

Abstract

Bifid scrotum is a rare congenital anomaly affecting the midline of the scrotum in a different spectra, in severe form the two scrotal sacs are widely separated with a laid opened urethra in the form of proximal hypospadias and the scrotal raphe is not detectable. Minor forms had a splitted or wide scrotal raphe and partial bifid scrotum may be seen at the proximal scrotal end or distally at the base of the scrotum, the later cases will give the look of scrotal dimple, which is a normal findings in some animals. Bifid scrota are usually associated with penoscrotal hypospadias, hypogonadism and androgen insensitivity syndrome, but it could be an isolated genital anomaly in association with rare somatic syndromes and maldevelopment. Bifid scrotum should be discussed along other related anomalies of the median raphae, perineal groove, accessory scrotum, scrotal transposition and diphallia. Embryologically the bifid scrotum is due to the lack of ventral growth of the caudal mesenchyme which causes failure of the urogenital folds to close over the cloacal membrane in the ventral midline. Selection of surgery to reconstruct scrotum is based on the severity of scrotal cleft and commonly done along hypospadias repair. Bifid scrotum reported recently as an indication for the severity of the associated hypospadias, and could determine the suitable type for its repair.

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Abbreviations

SSS:

Separation of the Scrotal Sac

AIS:

Androgen Insensitivity Syndrome

MR:

Median Raphae

VEG:

Virilization of the external genitalia

SMR:

Split Median Raphe

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Fahmy, M.A.B. (2022). Bifid Scrotum. In: Fahmy, M.A.B. (eds) Normal and Abnormal Scrotum. Springer, Cham. https://doi.org/10.1007/978-3-030-83305-3_14

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  • DOI: https://doi.org/10.1007/978-3-030-83305-3_14

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