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Cystic Fibrosis

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Physiology of Membrane Disorders

Abstract

Cystic fibrosis, an apparent inborn error of metabolism, is a common disease of children and young adults in countries with predominant Caucasian populations. It was first described by Fanconi in Switzerland following the recognition of the association of congenital cystic pancreatic fibrosis and bronchiectasis in 1936.(1) In this country, it was Andersen(2) who presented in 1938 the first complete description of the disease and introduced the term, “cystic fibrosis of the pancreas.” Although other names for the disease have been proposed in the past decades, the shortened form of the original name for the disease, “cystic fibrosis,” has become most common. A number of detailed reviews have recently appeared in the literature. (3–7)

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Author information

Authors and Affiliations

  1. Departments of Pediatrics, University of Florida Colleges of Medicine and Dentistry, Gainesville, Florida, 32610, USA

    John A. Mangos

  2. Department of Basic Dental Sciences, University of Florida Colleges of Medicine and Dentistry, Gainesville, Florida, 32610, USA

    John A. Mangos

  3. Division of Pulmonology and Cystic Fibrosis, University of Florida Colleges of Medicine and Dentistry, Gainesville, Florida, 32610, USA

    John A. Mangos

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  1. John A. Mangos
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Editor information

Editors and Affiliations

  1. Division of Nephrology, University of Alabama School of Medicine, Birmingham, Alabama, 35294, USA

    Thomas E. Andreoli M.D. (Professor of Medicine, Director, Professor of Physiology and Biophysics) (Professor of Medicine, Director, Professor of Physiology and Biophysics)

  2. Department of Physiology, Yale University School of Medicine, New Haven, Connecticut, 06510, USA

    Joseph F. Hoffman Ph.D. (Eugene Higgins Professor and Chairman) (Eugene Higgins Professor and Chairman)

  3. Division of Nephrology, University of California, San Diego, La Jolla, California, 92037, USA

    Darrell D. Fanestil M.D. (Professor of Medicine, Head) (Professor of Medicine, Head)

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© 1978 Plenum Publishing Corporation

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Mangos, J.A. (1978). Cystic Fibrosis. In: Andreoli, T.E., Hoffman, J.F., Fanestil, D.D. (eds) Physiology of Membrane Disorders. Springer, Boston, MA. https://doi.org/10.1007/978-1-4613-3958-8_44

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  • DOI: https://doi.org/10.1007/978-1-4613-3958-8_44

  • Publisher Name: Springer, Boston, MA

  • Print ISBN: 978-1-4613-3960-1

  • Online ISBN: 978-1-4613-3958-8

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