Skip to main content

Advertisement

Log in

Secondary Red Ear Syndrome in a Pediatric Patient: a Case Report

  • Case Report
  • Published:
SN Comprehensive Clinical Medicine Aims and scope Submit manuscript

Abstract

Red ear syndrome is a rare or underdiagnosed condition characterized by paroxysmal attacks of burning pain and reddening of the external ear. The pathophysiology is yet unclear, and few pediatric cases have been reported in the literature. Treatment remains one of the most challenging features of this condition.

An 8-year-old boy presented to the neurology department of the National Children’s Hospital, Caja Costarricense de Seguro Social, with a history of recurrent bilateral swelling of the external ears. Physical examination was remarkable for pain on palpation of the temporomandibular joint and wearing of the teeth, and a history of long-term bruxism could be elicited, leading to the diagnosis of secondary red ear syndrome.

Secondary pediatric red ear syndrome has rarely been reported in the literature. A thorough evaluation is essential to rule out secondary causes, and a multimodal treatment approach is advised due to the drug-resistant nature of this condition.

This is a preview of subscription content, log in via an institution to check access.

Access this article

Price excludes VAT (USA)
Tax calculation will be finalised during checkout.

Instant access to the full article PDF.

Institutional subscriptions

Fig. 1

Reproduced with permission from the patient and his mother

Fig. 2

Similar content being viewed by others

Data Availability

Not applicable.

Materials Availability

Not applicable.

Code Availability

Not applicable.

References

  1. D’Amico A, Galati C, Manzo ML, Reina F, Nocera GM, Raieli V. Red ear syndrome in children: review of literature and report of three cases. Int J Pediatr Otorhinolaryngol. 2021;142:110615. https://doi.org/10.1016/j.ijporl.2021.110615.

    Article  PubMed  Google Scholar 

  2. Lambru G, Miller S, Matharu MS. The red ear syndrome. J Headache Pain. 2013;14(1):83. https://doi.org/10.1186/1129-2377-14-83.

    Article  PubMed  PubMed Central  Google Scholar 

  3. Raieli V, Compagno A, D’Amelio M. Red ear syndrome. Curr Pain Headache Rep. 2016;20(3):19. https://doi.org/10.1007/s11916-016-0547-y.

    Article  CAS  PubMed  Google Scholar 

  4. Donnet A, Valade D. The red ear syndrome. J Neurol Neurosurg Psychiatry. 2004;75(7):1077. https://doi.org/10.1136/jnnp.2003.030742.

    Article  CAS  PubMed  PubMed Central  Google Scholar 

  5. Cinats AK, Haber RM. Pediatric red ear syndrome: a case report of an erythromelalgia type and review of the literature. Pediatr Dermatol. 2019;36(5):686–9. https://doi.org/10.1111/pde.13911.

    Article  PubMed  Google Scholar 

  6. Raieli V, Compagno A, Brighina F, La Franca G, Puma D, Ragusa D, et al. Prevalence of red ear syndrome in juvenile primary headaches. Cephalalgia. 2011;31(5):597–602. https://doi.org/10.1177/0333102410388437.

    Article  CAS  PubMed  Google Scholar 

  7. Raieli V, Giordano G, Spitaleri C, Consolo F, Buffa D, Santangelo G, et al. Migraine and cranial autonomic symptoms in children and adolescents: a clinical study. J Child Neurol. 2015;30(2):182–6. https://doi.org/10.1177/0883073814535494.

    Article  CAS  PubMed  Google Scholar 

  8. Ryan S, Wakerley BR, Davies P. Red ear syndrome: a review of all published cases (1996–2010). Cephalalgia. 2013;33(3):190–201. https://doi.org/10.1177/0333102412468673.

    Article  PubMed  Google Scholar 

  9. Lance JW. The red ear syndrome. Neurology. 1996;47(3):617–20. https://doi.org/10.1212/wnl.47.3.617.

    Article  CAS  PubMed  Google Scholar 

  10. Lee HS, Bae SC, Uhm WS, Jun JB, Lee IH, Kim SY. Red ear(s) syndrome associated with child neuropsychiatric systemic lupus erythematosus. Lupus. 2000;9(4):301–3. https://doi.org/10.1191/096120300680198908.

    Article  CAS  PubMed  Google Scholar 

  11. Bender SD. Orofacial pain and headache: a review and look at the commonalities. Curr Pain Headache Rep. 2014;18(3):400. https://doi.org/10.1007/s11916-013-0400-5.

    Article  PubMed  Google Scholar 

Download references

Author information

Authors and Affiliations

Authors

Contributions

Pilar Durán and Andrés Umaña were responsible for the acquisition of the data and drafted the initial manuscript, analyzed and interpreted the data, and reviewed and revised the manuscript. María del Carmen Navas and Adriana Ulate analyzed and interpreted the data for the work and reviewed and revised the manuscript. All authors approved the final manuscript as submitted and agree to be accountable for all aspects of the work.

Corresponding author

Correspondence to Andrés Umaña-Calderón.

Ethics declarations

Ethics Approval

Approval for the publication of this paper was granted by the Bioethics Department of the Caja Costarricense de Seguro Social, with the number CENDEISSS-AB-0589–2022.

Consent to Participate

Not applicable.

Consent for Publication

Informed consent was obtained from the mother of the patient, and informed assent was obtained from the patient for the presentation of this case, the pictures, and the test results.

Conflict of Interest

The authors declare no competing interests.

Additional information

Publisher's Note

Springer Nature remains neutral with regard to jurisdictional claims in published maps and institutional affiliations.

This article is part of the Topical Collection on Medicine

Rights and permissions

Springer Nature or its licensor (e.g. a society or other partner) holds exclusive rights to this article under a publishing agreement with the author(s) or other rightsholder(s); author self-archiving of the accepted manuscript version of this article is solely governed by the terms of such publishing agreement and applicable law.

Reprints and permissions

About this article

Check for updates. Verify currency and authenticity via CrossMark

Cite this article

Umaña-Calderón, A., Duran-Monge, P., del Carmen Navas-Aparicio, M. et al. Secondary Red Ear Syndrome in a Pediatric Patient: a Case Report. SN Compr. Clin. Med. 5, 8 (2023). https://doi.org/10.1007/s42399-022-01349-0

Download citation

  • Accepted:

  • Published:

  • DOI: https://doi.org/10.1007/s42399-022-01349-0

Keywords

Navigation