Abstract
Intracardiac paragangliomas most commonly arise from the left atrium and are often infiltrative and densely adherent to surrounding structures. Given their rarity, only scattered reports exist in the literature and standardized perioperative and surgical management is not well established. We describe a case of a 60-year-old woman with a mildly functioning intracardiac paraganglioma in which division of the superior vena cava improved exposure and enabled a complex limited resection. Further, we provide an overview of the diagnostic workup, perioperative medical management, surgical approach, and surveillance strategy in patients with these challenging tumors.
Similar content being viewed by others
References
Khan MF, Datta S, Chisti MM, Movahed MR. Cardiac paraganglioma: clinical presentation, diagnostic approach and factors affecting short and long-term outcomes. Int J Cardiol. 2013;166:315–20.
Chang CA, Pattison DA, Tothill RW, et al. 68 Ga-DOTATATE and 18 F-FDG PET/CT in Paraganglioma and Pheochromocytoma: utility, patterns and heterogeneity. Cancer Imaging. 2016;16:22.
Ramlawi B, David EA, Kim MP, et al. Contemporary surgical management of cardiac paragangliomas. Ann Thoracic Surg. 2012;93:1972–6.
Huo JL, Choi JC, DeLuna A, et al. Cardiac paraganglioma: diagnostic and surgical challenges. J Card Surg. 2012;27:178–82.
Brown ML, Zayas GE, Abel MD, Young WF Jr, Schaff HV. Mediastinal paragangliomas: the mayo clinic experience. Ann Thoracic Surg. 2008;86:946–51.
Funding
The authors received no financial support for the research, authorship, and/or publication of this article.
Author information
Authors and Affiliations
Corresponding author
Ethics declarations
Conflict of interest
The authors have no conflicts of interest related to the subject matter.
Ethical approval
The study has been approved by the Ethical Committee of our institution.
Informed Consent
All the subjects involved in the present study gave their consent to participate.
Consent to publication
All the subjects involved in the present study gave their consent to the publication of this document.
Additional information
Publisher's Note
Springer Nature remains neutral with regard to jurisdictional claims in published maps and institutional affiliations.
Electronic supplementary material
Below is the link to the electronic supplementary material.
Supplementary Video 1 Case details including workup, surgical approach, and techniques presented in a female patient with an intracardiac paraganglioma (MP4 185357 kb)
Rights and permissions
About this article
Cite this article
Guenthart, B.A., Trope, W., Keeyapaj, W. et al. Intracardiac paragangliomas: surgical approach and perioperative management. Gen Thorac Cardiovasc Surg 69, 555–559 (2021). https://doi.org/10.1007/s11748-020-01503-2
Received:
Accepted:
Published:
Issue Date:
DOI: https://doi.org/10.1007/s11748-020-01503-2