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Cochlear Implantation Outcomes of Cochlear Nerve Deficiency

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Cochlear Implantation for Cochlear Nerve Deficiency

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Abstract

Cochlear implantation (CI) is the primary intervention for patients with severe to profound sensorineural hearing loss. The mechanism of CI is to convert acoustic signals into electrical signals, directly stimulate the spiral ganglion (SGN), and transmit the signal to the auditory brainstem through the cochlear nerve (CN) fibers within the vestibulocochlear nerve (VCN). In patients with cochlear nerve deficiency (CND), the auditory brainstem can receive limited stimulation due to the reduced absolute number of CN fibers and the insufficient number of SGN. CND was once considered a contraindication to CI. In recent years, numerous studies have shown that patients with CND could benefit from CI. With advances in CI techniques, more patients with CND combined with inner ear malformation (IEM) are also included as indications for CI. This chapter describes CI outcomes in patients with CND with or without IEM and describes the role of radiological and electrophysiological factors in predicting hearing and speech outcomes after CI.

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Authors and Affiliations

  1. Department of Otorhinolaryngology Head and Neck Surgery, Beijing Tongren Hospital, Capital Medical University, Beijing, China

    Simeng Lu, Xingmei Wei, Ying Kong, Biao Chen, Lifang Zhang, Shujin Xue, Mengge Yang, Xinyue Zou, Xinyi Zhang & Yongxin Li

  2. Key Laboratory of Otolaryngology Head and Neck Surgery (Capital Medical University), Ministry of Education, Beijing, China

    Simeng Lu, Xingmei Wei, Ying Kong, Biao Chen, Lifang Zhang, Shujin Xue, Mengge Yang, Xinyue Zou, Xinyi Zhang & Yongxin Li

Authors
  1. Simeng Lu
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  2. Xingmei Wei
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  3. Ying Kong
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  4. Biao Chen
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  5. Lifang Zhang
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  6. Shujin Xue
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  8. Xinyue Zou
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  9. Xinyi Zhang
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  10. Yongxin Li
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Editors and Affiliations

  1. Capital Medical University, Beijing Tongren Hospital, Beijing, China

    Yongxin Li

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Lu, S. et al. (2022). Cochlear Implantation Outcomes of Cochlear Nerve Deficiency. In: Li, Y. (eds) Cochlear Implantation for Cochlear Nerve Deficiency. Springer, Singapore. https://doi.org/10.1007/978-981-19-5892-2_8

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  • DOI: https://doi.org/10.1007/978-981-19-5892-2_8

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  • Publisher Name: Springer, Singapore

  • Print ISBN: 978-981-19-5891-5

  • Online ISBN: 978-981-19-5892-2

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