Abstract
Moyamoya angiopathy (MMA) is an idiopathic, progressive intracranial occlusive vasculopathy leading to formation of abnormal vascular network of collaterals. Dural arteriovenous fistula (DAVF) has been rarely reported to co-exist with MMA. A paucity of literature has limited the elucidation of the pathophysiological association between the two conditions. It may be hypothesized that a chronic cerebral ischemic state in MMA and subsequent angiogenesis leading to the formation of collaterals might lead to the formation of DAVF. At present, there are no definite guidelines for treatment of DAVF in MMA. However, it may be reasonable to practice conservative management with close follow-up in case of asymptomatic DAVF or those without cerebral venous drainage, while high grade DAVF may be subjected to endovascular or open surgery to prevent future intracranial hemorrhage.
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Das, S., Dubey, S., Ray, B.K. (2022). Dural Arteriovenous Fistula in Moyamoya Angiopathy. In: Lv, X. (eds) Intracranial and Spinal Dural Arteriovenous Fistulas. Springer, Singapore. https://doi.org/10.1007/978-981-19-5767-3_14
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