Abstract
Dual outlet right ventricle (DORV) is a cardiac abnormality involving the outflow of the right ventricular system, the great arteries both originate from the right ventricle. Categorization of the group of abnormalities is based on the location of the VSD in relation to the aortic and pulmonary arteries. The location of the VSD has a significant impact on the physiologic symptoms of DORV as well as surgical concerns (subpulmonary, subaortic, committed, and non-committed VSD types). A comprehensive history of the patient’s illness and physical examination to assess the precordium and respiratory system should be used to identify clinically relevant heart abnormalities. Echocardiography typically gives enough information for a precise and appropriate diagnosis, as well as the information needed to design the surgical strategy. The pulmonary stenosis presence greatly influences the patient’s symptom profile and age at the time of clinical manifestation. Most of the patients were present earlier, in neonatal period. ECG, x-ray, cardiac angiography, and MRI were used but not standard or well-established diagnostic technique for this disease. CT scanning may be beneficial in determining coronary artery architecture in infants with TOF type. Medical and surgical treatment depends on the types of DORV and the associated anomalies. Palliative surgery can be done until the definitive treatment is possible. The prognosis also depends on whether the patient did a surgery or not, the type of intervention, and the underlying anomaly.
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Ahmad, M.S. (2023). Double Outlet Right Ventricle. In: Tagarakis, G., Gheni Sarfan, A., Hashim, H.T., Varney, J. (eds) Clinical and Surgical Aspects of Congenital Heart Diseases . Springer, Cham. https://doi.org/10.1007/978-3-031-23062-2_21
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DOI: https://doi.org/10.1007/978-3-031-23062-2_21
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