Abstract
Key features of orbital multiple myeloma (MM):
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Median age at diagnosis: 70 years
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Equal gender distribution
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Majority already diagnosed with MM
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Unilateral bony tumors (involving the sphenoid or frontal bone with orbital extension into the superior and superotemporal orbit)
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Other anatomical patterns include:
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1.
Discrete orbital tumors (mostly intraconal and adhering to an extraocular muscle)
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2.
Trans-spatial/multi-compartment lesions (e.g., sinuses, eyelids and facial soft tissues)
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1.
Imaging features on CT and MRI are variable:
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The greatest value in imaging is staging the local extent
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Enhancing soft tissue mass on CT with possible bony erosion, destruction or expansion
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Nonspecific MRI signal characteristics:
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T1-weighted images: isointense signal intensity to muscle
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T2-weighted images: intermediate to high signal intensity, often homogenous
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Post-contrast enhancement
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Restricted diffusion due to hypercellularity
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Aujla, J., Juniat, V., Patel, S., Selva, D. (2021). Orbital Multiple Myeloma. In: Ben Simon, G., Greenberg, G., Prat, D. (eds) Atlas of Orbital Imaging . Springer, Cham. https://doi.org/10.1007/978-3-030-41927-1_26-1
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DOI: https://doi.org/10.1007/978-3-030-41927-1_26-1
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