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Herlyn-Werner-Wunderlich Syndrome

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Atlas of Genetic Diagnosis and Counseling

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Abstract

Herlyn-Werner-Wunderlich syndrome (HWWS) (Herlyn and Werner 1971; Wunderlich 1976) is a rare Müllerian anomaly consisting of a didelphic uterus, a hemivaginal septum, and an ipsilateral renal agenesis. The diagnosis should be suspected in adolescent females with a pelvic mass and an ipsilateral renal agenesis.

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References

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Author information

Authors and Affiliations

  1. Medical Genetics, Shriners Hospitals for Children, Shreveport, LA, USA

    Harold Chen

  2. Perinatal and Clinical Genetics, Department of Pediatrics, LSU Health Sciences Center, 1501 Kings Highway, Shreveport, LA, 71130, USA

    Harold Chen

Authors
  1. Harold Chen
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Correspondence to Harold Chen .

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© 2016 Springer Science+Business Media New York

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Chen, H. (2016). Herlyn-Werner-Wunderlich Syndrome. In: Atlas of Genetic Diagnosis and Counseling. Springer, New York, NY. https://doi.org/10.1007/978-1-4614-6430-3_118-2

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  • DOI: https://doi.org/10.1007/978-1-4614-6430-3_118-2

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  • Publisher Name: Springer, New York, NY

  • Online ISBN: 978-1-4614-6430-3

  • eBook Packages: Springer Reference Biomedicine and Life SciencesReference Module Biomedical and Life Sciences

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