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Syringomyelia associated with Chiari I malformation

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Abstract

An 18-year-old man with progressive paraparesis, thermal hypoesthesia, sweating abnormalities, bladder dysfunction, severe orthostatic hypotension, bilateral Babinski sign, underwent a brain MRI scan that showed downward displacement of cerebellar tonsils through the foramen magnum, consistent with Chiari I malformation, compression of the brainstem–spinal cord junction, and C1–D11 syringomyelia (6.5 mm diameter at C2 level) consistent with Chiari I syndrome. Suboccipital craniectomy and duraplasty were performed. A C2 partial laminectomy and ablation of posterior arch of the atlas was performed. MRI scans 4 days and 1 month after surgery showed a dramatic syringomyelia reabsorption (2.5 and 1 mm, respectively) associated with complete clinical recovery.

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Correspondence to Chiara Briani.

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Lucchetta, M., Cagnin, A., Calderone, M. et al. Syringomyelia associated with Chiari I malformation. Neurol Sci 30, 525–526 (2009). https://doi.org/10.1007/s10072-009-0133-8

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  • DOI: https://doi.org/10.1007/s10072-009-0133-8

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