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Atrioventricular Septal Defects

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Cardiac CT and MR for Adult Congenital Heart Disease

Abstract

In normal heart, the real atrioventricular septum separates the morphological right atrium from the anatomic left ventricle. It has two portions; the anterosuperior is membranous and the posteroinferior is muscular. The latter is located between the mitral annulus and the tricuspid annulus. The peripheral atrioventricular junction is constituted by an extension of epicardial fat between the walls of atria and ventricles. In atrioventricular septal defect (AVSD) which is due to deficiency of myocardial tissue at AV junction, the membranous septum is absent and there is also a deficiency in the perimembranous muscular tissue. AVSD has received numerous designations in the past including endocardial cushion defect, persistent embryonic atrioventricular canal, atrioventricular canal defect, and ostium primum atrial septal defect. Defect of the endocardial atrioventricular cushions is a nonspecific designation since it can include the absence of right atrioventricular connection and double inlet left ventricle.

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Author information

Authors and Affiliations

  1. Department of Echocardiography, ABC Medical Center, National Institute of Cardiology Ignacio Chavez, Juan Badiano N° 1, Colonia Sección XVI, Tlalpan, Mexico City, 14080, Mexico

    Nilda Espinola-Zavaleta MD, PhD

  2. Department of Embryology, National Institute of Cardiology Ignacio Chavez, Mexico City, Mexico

    Luis Muñoz-Castellanos MD

  3. Department of Magnetic Resonance Imaging, National Institute of Cardiology Ignacio Chavez, Mexico City, Mexico

    Aloha Meave-Gonzalez MD

  4. Cardiovascular Magnetic Resonance Unit, National Institute of Cardiology Ignacio Chavez, Mexico City, Mexico

    Aloha Meave-Gonzalez MD

Authors
  1. Nilda Espinola-Zavaleta MD, PhD
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  2. Luis Muñoz-Castellanos MD
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  3. Aloha Meave-Gonzalez MD
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Corresponding author

Correspondence to Nilda Espinola-Zavaleta MD, PhD .

Editor information

Editors and Affiliations

  1. Department of Radiology, USC University Hospital Keck School of Medicine, Los Angeles, California, USA

    Farhood Saremi

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Espinola-Zavaleta, N., Muñoz-Castellanos, L., Meave-Gonzalez, A. (2014). Atrioventricular Septal Defects. In: Saremi, F. (eds) Cardiac CT and MR for Adult Congenital Heart Disease. Springer, New York, NY. https://doi.org/10.1007/978-1-4614-8875-0_14

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  • DOI: https://doi.org/10.1007/978-1-4614-8875-0_14

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