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Central Nervous System Vasculitis

Pathogenesis, Immunology, and Clinical Management

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Part of the book series: Current Clinical Neurology ((CCNEU))

Abstract

The vasculitides are a heterogenous group of multisystemic disorders that are pathologically characterized by inflammation of the blood vessels, structural damage to vessels, and usually vascular necrosis. Because involvement of blood vessels can result from inflammation of any type, vasculitis may be a presentation of diverse disorders. Vasculitis can occur either as a primary vasculitic disease or secondarily to another underlying pathology (13). Vasculitis of the nervous system is both a diagnostic and management challenge for clinicians. Both the central nervous system (CNS) and peripheral nervous system (PNS) may be involved in the vasculitic process.

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© 2005 Humana Press Inc., Totowa, NJ

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Mumtaz, S., Fowler, M.R., Gonzales-Toledo, E., Kelley, R.E. (2005). Central Nervous System Vasculitis. In: Minagar, A., Alexander, J.S. (eds) Inflammatory Disorders of the Nervous System. Current Clinical Neurology. Humana Press. https://doi.org/10.1385/1-59259-905-2:257

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  • DOI: https://doi.org/10.1385/1-59259-905-2:257

  • Publisher Name: Humana Press

  • Print ISBN: 978-1-58829-424-1

  • Online ISBN: 978-1-59259-905-9

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