Skip to main content

This is a preview of subscription content, log in via an institution to check access.

Access this chapter

Chapter
USD 29.95
Price excludes VAT (USA)
  • Available as PDF
  • Read on any device
  • Instant download
  • Own it forever
eBook
USD 189.00
Price excludes VAT (USA)
  • Available as EPUB and PDF
  • Read on any device
  • Instant download
  • Own it forever
Softcover Book
USD 249.99
Price excludes VAT (USA)
  • Compact, lightweight edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info
Hardcover Book
USD 329.99
Price excludes VAT (USA)
  • Durable hardcover edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info

Tax calculation will be finalised at checkout

Purchases are for personal use only

Institutional subscriptions

References

  1. Davis PB. Cystic Fibrosis since 1938. Am J Resp Crit Care Med 2006;173:475–82.

    Article  PubMed  Google Scholar 

  2. Ratjen F, Doring G. Cystic Fibrosis. Lancet 2003; 361:681–89.

    Article  PubMed  CAS  Google Scholar 

  3. Elborn JS, Bradley JM. Diagnosing CF: Sweat, blood and years. Thorax 2006;61:556–7.

    Article  PubMed  CAS  Google Scholar 

  4. Daftary A, Acton J, Heubi J et al. R. Fecal elastase-1: utility in pancreatic function in cystic fibrosis. J Cyst Fibros 2006;5:71–6.

    Article  PubMed  CAS  Google Scholar 

  5. Farrell PM, Kosorok MR, Rock MJ et al. Early diagnosis of cystic fibrosis through neonatal screening prevents severe malnutrition and improves long-term growth. Wisconsin Cystic Fibrosis Neonatal Screening Study Group. Pediatrics 2001;107:1–13.

    Article  PubMed  CAS  Google Scholar 

  6. Koscik RL, Farrell PM, Kosorok MR et al. Cognitive function of children with cystic fibrosis: deleterious effect of early malnutrition. Pediatrics 2004;113:1549–58.

    Article  PubMed  Google Scholar 

  7. Farrell PM, Li Z, Kosorok MR et al. Bronchopulmonary disease in children with cystic fibrosis after early or delayed diagnosis. Am J Respir Crit Care Med 2003;168:1100–8

    Article  PubMed  Google Scholar 

  8. Burke MS, Ragi JM, Karamanoukian HL et al. New strategies in non-operative management of meconium ileus. J Pediatr Surg 2002;37:760–4.

    Article  PubMed  Google Scholar 

  9. Yalcin E, Kiper N, Dogru D et al. Clinical features and treatment approaches to cystic fibrosis with pseudo-bartter syndrome. Ann Trop Paed 2005;25:119–4.

    Article  Google Scholar 

  10. Escobar M, Grosfeld J, Burdick J et al. Surgical considerations in cystic fibrosis. Surgery 2005;138:560–72.

    Article  PubMed  Google Scholar 

  11. Minasian CC, Sriskandan S, Balfour-Lynn IM et al. Cystic fibrosis presenting with haematological abnormalities. Clin Lab Haematol 2006;28:423–6.

    Article  PubMed  CAS  Google Scholar 

  12. Phillips RJ, Crock CM, Dillon MJ et al. Cystic fibrosis presenting as kwashiorkor with florid skin rash. Arch Dis Child 1993;69:446–8.

    Article  PubMed  CAS  Google Scholar 

  13. Ranganathan SC, Dezateux C, Bush A et al. London Collaborative Cystic Fibrosis Group. Airway function in infants newly diagnosed with cystic fibrosis. Lancet 2001;358:1964–5.

    CAS  Google Scholar 

  14. Balfour-Lynn IM, Elborn S. Respiratory infection. In: Hodson M, Geddes D, Bush A (eds) 3rd ed. Cystic fibrosis. London: Arnold; 2007.

    Google Scholar 

  15. Smyth A, Walters S. Prophylactic anti-staphylococcal antibiotics for cystic fibrosis. Cochrane Database of Systematic Reviews 2003, Issue 3. Art. No.: CD001912. DOI: 10.1002/14651858. CD001912.

    Google Scholar 

  16. Davies JC. Pseudomonas aeruginosa in cystic fibrosis: pathogenesis and persistence. Paed Resp Rev 2002;3:128–34.

    Article  Google Scholar 

  17. Ryan G, Mukhopadhyay S, Singh M. Nebulised antipseudomonal antibiotics for cystic fibrosis. Cochrane Database of Systematic Reviews 2003, Issue 3. Art. No.: CD001021. DOI: 10.1002/14651858.CD001021.

    Google Scholar 

  18. Goss CH, Otto K, Aitken M et al. Detecting Stenotrophomonas maltophilia does not reduce survival of patients with cystic fibrosis. Am J Resp Crit Care Med 2002;166:356–61.

    Article  PubMed  Google Scholar 

  19. Speert DP. Advances in Burkholderia cepacia complex. Paed Resp Rev 2002;3:230–5.

    Article  Google Scholar 

  20. Olivier KN. The natural history of non-tuberculosis mycobacteria in patients with cystic fibrosis. Paed Resp Rev 2004;5 (Suppl A): S213–S216.

    Article  Google Scholar 

  21. Samuels S. Physiotherapy for children with cystic fibrosis. Paed Resp Rev 2000;1:190–196.

    Article  CAS  Google Scholar 

  22. Balfour-Lynn IM, Elborn S. “CF asthma”: what is it and what do we do about it? Thorax 2002;57:742–8.

    Article  PubMed  CAS  Google Scholar 

  23. Jaffe A, Balfour-Lynn IM. Treatment of severe small airways disease in children with cystic fibrosis: alternatives to corticosteroids. Paed Drugs 2002;4:381–9.

    Google Scholar 

  24. Jones AP, Wallis CE, Kearney CE. Recombinant human deoxyri-bonuclease for cystic fibrosis. Cochrane Database of Systematic Reviews 2003, Issue 3. Art. No.: CD001127. DOI: 10.1002/14651858. CD001127.

    Google Scholar 

  25. Elkins MR, Robinson M, Rose BR et al. A controlled trial of long-term inhaled hypertonic saline in patients with cystic fibrosis. NEJM 2006;354: 229–40.

    Article  PubMed  CAS  Google Scholar 

  26. Southern KW, Barker PM, Solis A. Macrolide antibiotics for cystic fibrosis. Cochrane Database of Systematic Reviews 2004, Issue 2. Art. No.: CD002203. DOI: 10.1002/14651858.CD002203.pub2.

    Google Scholar 

  27. Mastella G, Rainisio M, Harms HK et al. Allergic bronchopul-monary aspergillosis in cystic fibrosis. A European epidemiological study. Epidemiologic Registry of Cystic Fibrosis. Eur Respir J 2000;16:464–71.

    CAS  Google Scholar 

  28. Stevens DA, Moss RB, Kurup VP et al; Participants in the Cystic Fibrosis Foundation Consensus Conference. Allergic bron-chopulmonary aspergillosis in cystic fibrosis–state of the art: Cystic Fibrosis Foundation Consensus Conference. Clin Infect Dis 2003;37 Suppl 3:S225–S264.

    Article  PubMed  Google Scholar 

  29. Henry M, Arnold T, Harvey J; Pleural Diseases Group, Standards of Care Committee, British Thoracic Society. BTS guidelines for the management of spontaneous pneumothorax. Thorax 2003;58 Suppl 2:ii39–ii52.

    Article  PubMed  Google Scholar 

  30. Cutis HJ, Bourke SJ, Dark JH et al. Lung transplantation outcome in cystic fibrosis patients with previous pneumothorax. J Heart Lung Transp 2005;24:865–9.

    Article  Google Scholar 

  31. Flume PA, Yankasas JR, Ebeling M et al. Massive haemoptysis in cystic fibrosis. Chest 2005;128:729–38.

    Article  PubMed  Google Scholar 

  32. Clinical guidelines for the care of children with cystic fibrosis. Royal Brompton Hospital. 2007 4th Edition. www.rbht.nhs.uk/ childrencf

    Google Scholar 

  33. Lucas J, Connett GJ, Lea R et al. Lung resection in cystic fibrosis patients with localised pulmonary disease. Arch Dis Child 1996;74:449–51.

    Article  PubMed  CAS  Google Scholar 

  34. Lucas JS, Connett GJ, Fairhurst J. Long term results of lung resection in cystic fibrosis patients with localised lung disease. Arch Dis Child 2002;86:66.

    Article  PubMed  CAS  Google Scholar 

  35. Littlewood JM, Wolfe SP, Conway SP. Diagnosis and treatment of intestinal malabsorption in cystic fibrosis. Pediatr Pulmonol 2006;41:35–49.

    Article  PubMed  Google Scholar 

  36. Navarro J, Rainisio M, Harms HK et al. Factors associated with poor pulmonary function: cross-sectional analysis of data from the ERCF. Eur Resp J 2001;18:298–305.

    Article  CAS  Google Scholar 

  37. Heine R, Button B, Olinsky A et al. Gastro-oesophageal reflux in infants under 6 months with cystic fibrosis. Arch Dis Child 1998;78:44–8.

    Article  PubMed  CAS  Google Scholar 

  38. Chaudry G, Navarro O, Levine D et al. Abdominal manifestations of cystic fibrosis in children. Pediatr Radiol 2006;36:233–40.

    Article  PubMed  Google Scholar 

  39. Taylor CJ, Aswani N. The pancreas in cystic fibrosis. Ped Resp Rev 2002;3:77–81

    Article  CAS  Google Scholar 

  40. Diwakar V, Pearson L, Beath S. Liver disease in children with cystic fibrosis. Paed Resp Rev 2001;2:340–9.

    Article  CAS  Google Scholar 

  41. Cheng K, Ashby D, Smyth R. Ursodeoxycholic acid for cystic fibrosis-related liver disease. Cochrane Database of Systematic Reviews 1999, Issue 3. Art. No.: CD000222. DOI: 10.1002/14651858.CD000222.

    Google Scholar 

  42. Milla C, Warwick W, Moran A. Trends in pulmonary function in patients with cystic fibrosis correlate with the degree of glucose intolerance at baseline. Am J Resp Crit Care Med 2000;162:891–5.

    PubMed  CAS  Google Scholar 

  43. Aris R, Lester G, Ontjes D. Treatment of bone disease in cystic fibrosis. Curr Opin Pulm Med 2004;10:524–30.

    Article  PubMed  Google Scholar 

  44. Botton E, Saraux A, Laselve H et al. Musculoskeletal manifestations in cystic fibrosis. Joint Bone Spine 2003;70:327–35.

    Article  PubMed  Google Scholar 

  45. Lyon A, Bilton D. Fertility issues in cystic fibrosis. Paed Res Rev 2002;3:236–40.

    Article  Google Scholar 

  46. Prasad SA, Balfour-Lynn IM, Carr SB et al. A comparison of the prevalence of urinary incontinence in girls with cystic fibrosis, asthma and healthy controls. Pediatr Pulmonol 2006;41:1065–8.

    Article  PubMed  CAS  Google Scholar 

  47. Balfour-Lynn IM, Malbon K, Burman JF et al. Thrombophilia in children with cystic fibrosis. Pediatr Pulmonol 2005;39:306–10.

    Article  PubMed  CAS  Google Scholar 

  48. A-Rahman A, Spencer D. Totally implantable vascular access devices for cystic fibrosis. Cochrane Database of Systematic Reviews 2003, Issue 3. Art. No.: CD004111. DOI: 10.1002/14651858. CD004111.

    Google Scholar 

  49. Munck A, Malbezin S, Bloch J et al. Follow-up of 452 totally implantable vascular devices in cystic fibrosis patients. Eur Resp J 2004;23:430–4.

    Article  CAS  Google Scholar 

  50. Burch M, Aurora P. Current status of paediatric heart, lung, and heart-lung transplantation Arch Dis Child 2004; 89:386–9.

    Article  PubMed  CAS  Google Scholar 

  51. Webber SA, McCurry K, Zeevi A. Heart and lung transplantation in children. Lancet 2006;368:53–69.

    Article  PubMed  Google Scholar 

  52. Rowe SM, Clancy JP. Advances in cystic fibrosis therapies. Curr Opin Pediatr 2006;18:604–13.

    Article  PubMed  Google Scholar 

Download references

Author information

Authors and Affiliations

Authors

Editor information

Editors and Affiliations

Rights and permissions

Reprints and permissions

Copyright information

© 2009 Springer-Verlag London Limited

About this chapter

Cite this chapter

Brown, S., Balfour-Lynn, I.M. (2009). Cystic Fibrosis. In: Parikh, D.H., Crabbe, D.C.G., Auldist, A.W., Rothenberg, S.S. (eds) Pediatric Thoracic Surgery. Springer, London. https://doi.org/10.1007/b136543_35

Download citation

  • DOI: https://doi.org/10.1007/b136543_35

  • Publisher Name: Springer, London

  • Print ISBN: 978-1-84800-902-8

  • Online ISBN: 978-1-84800-903-5

  • eBook Packages: MedicineMedicine (R0)

Publish with us

Policies and ethics