Abstract
Intraosseous malignant peripheral nerve sheath tumor (IMPNST) is a malignant tumor of bone arising from peripheral nerve sheath cells. It usually develops secondarily by malignant transformation in pre-existing neurofibromas, schwannomas, or following radiation therapy. However, IMPNST can extraordinarily occur primarily from the nerves within the bone.
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Bahk, WJ. (2023). Malignant Peripheral Nerve Sheath Tumor. In: Diagnosis and Management of Primary Bone Tumors. Springer, Singapore. https://doi.org/10.1007/978-981-99-5498-8_23
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DOI: https://doi.org/10.1007/978-981-99-5498-8_23
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