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Understanding Syringomyelia and Chiari Malformations

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A Practical Guide to Care of Spinal Cord Injuries

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Abstract

Syringomyelia is a complex neurological condition characterized by the presence of a fluid-filled cavity within the spinal cord. While it is not a standalone disease, it is often associated with other underlying pathological processes. One such condition is Chiari malformation, which is characterized by the herniation of the cerebellar tonsils through the foramen magnum and into the cervical spinal canal. This chapter explores the relationship between these two conditions, with an emphasis on posttraumatic syringomyelia. The symptoms of syringomyelia are diverse and can include sensory deficits, pain, weakness, stiffness, and disruptions to sweating, sexual function, and bladder and bowel control. The progression of the disease can be unpredictable, with an initial rapid decline followed by a more gradual deterioration. The increased use of magnetic resonance imaging (MRI) has helped to enhance the detection of syringomyelia. The chapter provides an in-depth understanding of posttraumatic syringomyelia and its association with Chiari malformation in the context of spinal cord injuries. Posttraumatic syringomyelia can occur following a spinal cord injury, and it is important for healthcare providers to be aware of this possibility and to monitor patients for symptoms. The chapter also covers the pathophysiology, diagnosis, and treatment options for syringomyelia, with a focus on the management of posttraumatic syringomyelia in patients with spinal cord injuries. Overall, this chapter provides a comprehensive overview of syringomyelia and its association with Chiari malformation in the context of spinal cord injuries.

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Authors and Affiliations

  1. Parkside Rehabilitation Hospital, Busan, Korea (Republic of)

    Hyun-Yoon Ko

  2. Department of Rehabilitation Medicine, Pusan National University College of Medicine, Yangsan, Korea (Republic of)

    Hyun-Yoon Ko

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  1. Hyun-Yoon Ko
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Ko, HY. (2023). Understanding Syringomyelia and Chiari Malformations. In: A Practical Guide to Care of Spinal Cord Injuries. Springer, Singapore. https://doi.org/10.1007/978-981-99-4542-9_20

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  • DOI: https://doi.org/10.1007/978-981-99-4542-9_20

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  • Publisher Name: Springer, Singapore

  • Print ISBN: 978-981-99-4541-2

  • Online ISBN: 978-981-99-4542-9

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