Robotic System Assisted Soave Procedure for Hirschsprung Disease

Abstract

Hirschsprung disease (HSCR), also known as “congenital megacolon” or “aganglionosis,” is caused by the absence of ganglion cells in the Auerbach and Meissner plexuses of the affected bowel. Patients with Hirschsprung disease present with delayed passage of meconium beyond the first 24 h, chronic severe constipation, abdominal distention, failure to thrive, and dependence on enemas to maintain defecation. Plain radiographs characteristically show dilated bowel loops throughout the abdomen. Typical finding of contrast enema in patient of HSCR is the obvious stenotic distal bowel and dilated proximal bowel, and retention of the contrast 24 h later on plain radiograph. Rectal biopsy is the gold standard for the diagnosis of HSCR, by suction rectal biopsy or full-thickness biopsy. Anorectal manometry is another useful screening technique.