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Syndromic Wilms’ Tumor

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Wilms’ Tumor

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Abstract

Wilms’ tumor (WT) is known to be associated with various genetic syndromes and several distinct clinical conditions. This chapter will highlight the epidemiology, incidence, and burden of disease of syndromic WT and their association with various genetic and clinical abnormalities. The learning points will focus on identifying these at-risk patients, with guidelines for screening and follow-up, tailored medical and surgical therapy in these patients, and long-term effects and considerations of transition care to adulthood in this group.

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Authors and Affiliations

  1. Department of Pediatric Surgery, Post Graduate Institute of Medical Education and Research, Chandigarh, India

    Nitin James Peters & Ram Samujh

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  1. Nitin James Peters
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  2. Ram Samujh
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Editors and Affiliations

  1. Department of Pediatric Surgery, Lady Hardinge Medical College and Kalawati Saran Children’s Hospital, New Delhi, India

    Yogesh Kumar Sarin

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Peters, N.J., Samujh, R. (2022). Syndromic Wilms’ Tumor. In: Sarin, Y.K. (eds) Wilms’ Tumor. Springer, Singapore. https://doi.org/10.1007/978-981-19-3428-5_5

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  • DOI: https://doi.org/10.1007/978-981-19-3428-5_5

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