Abstract
Hypo-enhancement of solid hepatic tumors in the portal venous and late phases is the most important contrast-enhanced ultrasound (CEUS) feature for detecting malignant hepatic tumors, and contrast-enhanced ultrasound can significantly improve the detection of malignant liver tumors. This chapter will introduce conventional ultrasound and CEUS features of rare malignant liver tumors, including lymphoma, combined hepatocellular, and cholangiocarcinoma, fibrolamellar hepatocellular carcinoma, hepatic cystadenocarcinoma, neuroendocrine tumor, and hepatic epithelioid hemangioendothelioma. For some rare malignant liver tumors, surgery may not the first choice or unique therapeutic method. Further details of arterial phase enhancement patterns and the timing, degree, and patterns of washout combined with conventional ultrasound features may be helpful for diagnosis in order to guide clinical therapy selection.
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Abbreviations
- 18F-FDG-EPT/CT:
-
Fluorine-18-fluorodeoxyglucose positron emission tomography/computed tomography
- CCA:
-
Cholangiocarcinoma
- CDFI:
-
Color Doppler flow imaging
- CEUS:
-
Contrast enhanced ultrasound
- cHCC-CCA:
-
Combined hepatocellular carcinoma and cholangiocarcinoma
- CT:
-
Computed tomography
- DLBCL:
-
Diffuse large B cell lymphoma
- f-HCC:
-
Fibrolamellar hepatocellular carcinoma
- FLL:
-
Focal liver lesion
- HAS:
-
Hepatic angiosarcoma
- HBCAC:
-
Hepatic biliary cystadenocarcinoma
- HBCT:
-
Hepatic biliary cystic tumor
- HCC:
-
Hepatocellular carcinoma
- HEHE:
-
Hepatic epithelioid hemangioendothelioma
- HL:
-
Hodgkin lymphoma
- HNEN:
-
Hepatic neuroendocrine neoplasm
- ICC:
-
Intrahepatic cholangiocarcinoma
- MHNEN:
-
Metastatic hepatic neuroendocrine neoplasm
- MRI:
-
Magnetic resonance image
- NEN:
-
Neuroendocrine neoplasm
- NHL:
-
Non-Hodgkin lymphoma
- PHL:
-
Primary hepatic lymphoma
- PHNEN:
-
Primary hepatic neuroendocrine neoplasm
- US:
-
Ultrasound
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Lu, Q., Fan, PL., Dong, Y., Cao, JY., Wang, WP. (2021). Rare Malignant Liver Tumors. In: Wang, WP., Dong, Y., Dietrich, C.F., Jung, E.M. (eds) Contrast-Enhanced Ultrasound Imaging of Hepatic Neoplasms. Springer, Singapore. https://doi.org/10.1007/978-981-16-1761-4_6
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