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Rare Malignant Liver Tumors

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Contrast-Enhanced Ultrasound Imaging of Hepatic Neoplasms
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Abstract

Hypo-enhancement of solid hepatic tumors in the portal venous and late phases is the most important contrast-enhanced ultrasound (CEUS) feature for detecting malignant hepatic tumors, and contrast-enhanced ultrasound can significantly improve the detection of malignant liver tumors. This chapter will introduce conventional ultrasound and CEUS features of rare malignant liver tumors, including lymphoma, combined hepatocellular, and cholangiocarcinoma, fibrolamellar hepatocellular carcinoma, hepatic cystadenocarcinoma, neuroendocrine tumor, and hepatic epithelioid hemangioendothelioma. For some rare malignant liver tumors, surgery may not the first choice or unique therapeutic method. Further details of arterial phase enhancement patterns and the timing, degree, and patterns of washout combined with conventional ultrasound features may be helpful for diagnosis in order to guide clinical therapy selection.

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Abbreviations

18F-FDG-EPT/CT:

Fluorine-18-fluorodeoxyglucose positron emission tomography/computed tomography

CCA:

Cholangiocarcinoma

CDFI:

Color Doppler flow imaging

CEUS:

Contrast enhanced ultrasound

cHCC-CCA:

Combined hepatocellular carcinoma and cholangiocarcinoma

CT:

Computed tomography

DLBCL:

Diffuse large B cell lymphoma

f-HCC:

Fibrolamellar hepatocellular carcinoma

FLL:

Focal liver lesion

HAS:

Hepatic angiosarcoma

HBCAC:

Hepatic biliary cystadenocarcinoma

HBCT:

Hepatic biliary cystic tumor

HCC:

Hepatocellular carcinoma

HEHE:

Hepatic epithelioid hemangioendothelioma

HL:

Hodgkin lymphoma

HNEN:

Hepatic neuroendocrine neoplasm

ICC:

Intrahepatic cholangiocarcinoma

MHNEN:

Metastatic hepatic neuroendocrine neoplasm

MRI:

Magnetic resonance image

NEN:

Neuroendocrine neoplasm

NHL:

Non-Hodgkin lymphoma

PHL:

Primary hepatic lymphoma

PHNEN:

Primary hepatic neuroendocrine neoplasm

US:

Ultrasound

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Lu, Q., Fan, PL., Dong, Y., Cao, JY., Wang, WP. (2021). Rare Malignant Liver Tumors. In: Wang, WP., Dong, Y., Dietrich, C.F., Jung, E.M. (eds) Contrast-Enhanced Ultrasound Imaging of Hepatic Neoplasms. Springer, Singapore. https://doi.org/10.1007/978-981-16-1761-4_6

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  • DOI: https://doi.org/10.1007/978-981-16-1761-4_6

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