Health-Care Transition for Patients with Allied Disorders of Hirschsprung’s Disease

  • Hideki SohEmail author


For young patients to receive medical care in accordance with age-related changes in physical condition and complications and physical and personality maturity, the health-care transition from childhood to adult appropriate medical care is an important subject. However, allied disorders of Hirschsprung’s disease are rare and severe condition, so it is not easy to progress the transition to an adult health-care system. In this condition medical care should be seamlessly continued from childhood to adulthood, and it is necessary to prepare programs including seamless diagnostic criteria, severity classification, guidelines, education, and guidance of medical support.


Allied disorders of Hirschsprung’s disease Isolated hypoganglionosis Chronic intestinal pseudo-obstruction (CIPO) Megacystis microcolon intestinal hypoperistalsis syndrome (MMIHS) Health-care transitions Home parenteral nutrition 


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© Springer Nature Singapore Pte Ltd. 2019

Authors and Affiliations

  1. 1.Department of Pediatric SurgeryOsaka Women’s and Children’s HospitalIzumiJapan

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