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Epidemiology

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Gastrointestinal Stromal Tumor

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Abstract

GIST is a rare tumor, but determining its incidence is a challenge. Incidence from prior reports ranges from 0.43 to 2.2 per 100,000, but the reports that examined stomach specimen from autopsy or surgery of other diseases suggest that there may be occult GISTs. The distinction between benign and malignant cases is also ambiguous. Cancer registries may not be a reliable source because many limit the reportability of the tumor into only malignant cases. An analysis using hospital-based cancer registries in Japan suggests that overtly malignant cases are about one third of cases that are considered as at least some malignancy (labeled as /1 or /3 in the behavior code of ICD-O-3). We do not know how many cases are there that are considered as benign. Some summaries of the current status of GIST treatment are provided using the same dataset.

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Authors and Affiliations

  1. Center for Cancer Registries, National Cancer Center, Tokyo, Japan

    Takahiro Higashi

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  1. Takahiro Higashi
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Correspondence to Takahiro Higashi .

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Editors and Affiliations

  1. Department of Gastroenterological Surgery, Osaka University Graduate School of Medicine, Osaka, Japan

    Yukinori Kurokawa

  2. Department of Cancer Chemotherapy, Hokkaido University Hospital Cancer Center, Sapporo, Hokkaido, Japan

    Yoshito Komatsu

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© 2019 Springer Nature Singapore Pte Ltd.

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Higashi, T. (2019). Epidemiology. In: Kurokawa, Y., Komatsu, Y. (eds) Gastrointestinal Stromal Tumor. Springer, Singapore. https://doi.org/10.1007/978-981-13-3206-7_1

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  • DOI: https://doi.org/10.1007/978-981-13-3206-7_1

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  • Publisher Name: Springer, Singapore

  • Print ISBN: 978-981-13-3205-0

  • Online ISBN: 978-981-13-3206-7

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