Abstract
Congenital absence of vagina is often associated with no uterus or only a primordial uterus, while the fallopian tubes and ovaries develop normally. Patients will have secondary sexual characteristics of a normal female. Their karyotype is 46XX and is known as the Mayer-Rokitansky-Küster-Hauser syndrome (MRKH). The incidence of MRKH is 1/5000 to 1/4000. China is a country of very large population, with an estimated 15 million patients suffering from MRKH. Many of them are living in rural areas and are not being diagnosed. For 11 years from 1986 to 1996, Tianjin City Centre Obstetrics and Gynecology Hospital had treated 109 patients of congenital absence of vagina, about 0.6 % of the total gynecologic inpatients in the same period. At the same time, from January 2003 to November 2013, the Shenzhen Luohu Hospital had treated 659 patients with congenital absence of vagina, accounting for 2.3 % of 28,364 gynecological inpatients in the same period.
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Luo, G. et al. (2015). Abnormal Development of the Vagina. In: Zhu, L., Wong, F., Lang, J. (eds) Atlas of Surgical Correction of Female Genital Malformation. Springer, Dordrecht. https://doi.org/10.1007/978-94-017-7246-4_4
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DOI: https://doi.org/10.1007/978-94-017-7246-4_4
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